Introduction:

Klippel-Trenaunay syndrome is a rare congenital disease characterized by a classic triad consisting of a cutaneous capillary malformation, hypertrophy of soft tissue and/or bone in the limbs, and venous malformations, resulting in varicose veins or other malformations of the deep venous system.

Objective:

To present sclerotherapy as a therapeutic option in the management of Klippel-Trenaunay syndrome.

Methods:

It is presented the case of a 27-year-old female patient, with white skin, a history of diagnosis of Klippel-Trenaunay syndrome since she was three years old, which manifested as a nevus from birth, located in the left gluteal region, increased size of the limb and presence of venous dilations since early childhood.

Results:

Foam sclerotherapy was used as a treatment for varicose veins.

Conclusions:

Varicose tracts were eliminated, which improved the aesthetics and functionality of the limb.