Resumen

BARAJAS GOMEZ, Teresa de Jesús et al. Klippel-Trenaunay Syndrome. Rev Cubana Med Gen Integr [online]. 2016, vol.32, n.3, pp. 0-0. ISSN 1561-3038.

Klippel - Trenaunay -Weber congenital vascular malformation characterized by a triad of clinical manifestations comprising a venular, venous and lymphatic vascular malformation, with hypertrophy increased skeletal and soft tissue of one or more members. Of unknown etiology, it is believed to pathogenically an alteration occurs in mesoderm development in the fetus, which affects angioblastic , and osteoblastic lymphoblastoid lines. Is presentedthe case of a 5 year old that has a vascular malformation, initially diagnosed as vascular hemangioma and later was associated with Klippel- Trenaunay -Weber.Objective: To generate knowledge about the clinical features of KlippelTrenaunay Syndrome for diagnosis and treatment.

Palabras clave : Klippel-Trenaunay syndrome; hypertrophy; angiodysplasia.

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