Introduction:

spinocerebellar ataxia type 2 is an autosomal dominant inherited disease in which degeneration of the cerebellum and its afferent and efferent pathways occurs and is characterized by ataxia, dysarthria, dysmetria, adiadochokinesia, action tremor, painful muscle contractures, early neuropathy, nystagmus, pyramidal signs, and cognitive, sleep and autonomic disorders.

Patient information:

anesthetic management is reported in a patient in which the main implications of anesthesia are related to neuromuscular degeneration and the possible occurrence of respiratory complications.

Conclusions:

the adequate selection of anesthetic agents, the use of non-depolarizing muscle relaxants in reduced doses, epidural anesthesia combined with general anesthesia, early removal of the endotracheal tube or laryngeal mask, early mobilization and neuromuscular and cardiorespiratory monitoring are the fundamental elements in the anesthetic management of this patient.

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