Resumen

CRISTOBO BRAVO, Tania; LACOSTE PINAR, María Josefa; SALELLAS BRINGUEZ, Julieta  y  GONZALEZ SAEZ, Yoandra. Polyarteritis nodosa in children: first case report in Camagüey. AMC [online]. 2012, vol.16, n.4, pp. 490-500. ISSN 1025-0255.

Background: polyarteritis nodosa is a vasculitis of medium-sized vessels, characterized by inflammation or necrosis of blood vessels leading to occlusion and therefore to ischemia of tissue supplying.      Case report: 15 years old, white, male patient with history of long febrile pictures without diagnosis, he had multiple admissions in different institutions in the country with the suspicion of histiocytosis or lymphoproliferative disease, various studies involving bone marrow without infiltration and lymph node biopsy were performed, results ruled out these diseases.  In one of these episodes and three years later was referred to the Pediatric Rheumatology service in Camagüey province, with history of fever up to 38.5 ° c for 16 days, an ulcer infected with a staphylococcus in the same culture on the right arm. After his examination also was found Raynaud´s phenomenon and livedo reticularis, a diagnostic possibility of vasculitis was suggested.     Conclusions: the antinuclear antibodies carried out were positive and confirmed diagnosis of polyarteritis nodosa, which was made after three years of evolution; currently under treatment of extreme immunosuppression with high doses of steroids and cyclophosphamide with favorable evolution of the general picture, no fever, but remains damage at the level of renal, coronary vessels and distal regions of four extremities established previously.

Palabras clave : POLYARTERITIS NODOSA; RAYNAUD DISEASE; ADOLESCENT; IMMUNOSUPPRESSION; CASE STUDIES.

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