Introduction:

Systemic sclerosis is a rare disease for which there is limited information in the Reference Center for Rheumatic Diseases of Havana.

Objective:

To describe the clinical manifestations of patients treated with this diagnosis in the period from November 2017 to March 2019.

Methods:

A descriptive, cross-sectional observational study was carried out in 73 patients. Sociodemographic variables such as age, sex and skin color and clinical variables such as form of presentation, time of diagnosis of the disease and clinical manifestations by organs and systems were evaluated.

Results:

57.5 % presented the diffuse form of the disease and 48.8 % had more than 10 years of diagnosis. Skin involvement was the most frequent with 98.6 %; thickening and hardening of the skin predominated. The digestive affection followed it in order of frequency, with 94.5 % with a predominance of peptic ulcer. Osteomyoarticular was the third most frequent with 89.0 %, where arthralgia and arthritis had more representation. Cardiac and vascular manifestations affected 87.7 % of all patients; within the first, rhythm disturbances were present in 73.9 % and in the second, Raynaud's phenomenon was observed in 80.8 %.

Conclusions:

The diffuse form of the disease predominated, patients with more than 10 years of diagnosis and cutaneous, digestive, osteomyoarticular and cardiac and vascular involvement.

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