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Revista Cubana de Medicina
versão On-line ISSN 1561-302X
Resumo
PINO ALFONSO, Pedro Pablo e HERNANDEZ MORENO, Laura. Pulmonary lymphangioleiomyomatosis. Rev cubana med [online]. 2020, vol.59, n.4 Epub 15-Nov-2020. ISSN 1561-302X.
Introduction:
Pulmonary lymphangioleiomyomatosis constitutes a challenge, both in its diagnostic management and in the care of complications. It is a rare disease characterized by the proliferation of smooth muscle around the bronchovascular and lymphatic structures and in the pulmonary interstitium, together with cystic dilation of the terminal air spaces.
Objective:
To describe a diagnosed case of pulmonary lymphangioleiomyomatosis.
Case report:
A case of pulmonary lymphangioleiomyomatosis is reported, which was clinically showed as recurrent pneumothorax. A definitive diagnosis was reached by performing a lung biopsy.
Discussion:
Lymphangioleiomyomatosis is a rare entity that mainly affects women of childbearing age and is characterized by the presence of a diffuse cystic pattern. Its prevalence and incidence is unknown.
Conclusions:
It can be concluded that the presence of spontaneous or recurrent pneumothorax in a woman of childbearing age, or pregnant, should be suspected lymphangioleiomyomatosis.
Palavras-chave : lymphangioleiomyomatosis; lung tumor; pneumothorax.