Resumo

CAPOTE PEREIRA, Lázaro L. et al. Bronchiobiliary fistula. Rev Cub Med Mil [online]. 2006, vol.35, n.2, pp. 0-0. ISSN 1561-3046.

Autosomal dominant polycystic kidney disease (PKD-1) is the most frequent inherited nephropathy and constitutes an important cause of terminal chronic kidney failure. Bronchiobiliary fistula is a rare complication secondary to infections like granular Equinococcus and amebiasis, trauma and malignant disease. Frequent manifestations of this disease are bile expectoration (biliphthisis) and respiratory symptoms. The case of a 65 years-old Caucasian female patient suffering from PKD-1 and chronic kydney failure, with respiratory symptoms and biliphthisis secondary to a bronchiobiliary fistula was presented. The diagnosis was confirmed with the demonstration of the fistulous path in the hepatic parenchyma and the presence of bile in the pulmonary parenchyma by means of Fouchet´s stain. It was concluded that PKD-1 is a rare cause of bronchiobiliary fistula and a diagnosis that must be added to the already known causes of this complication.

Palavras-chave : Autosomal dominant polycystic kidney disease (PKD-1); bronchiobiliary fistula; biliphthisis; chronic kidney failure.

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