Resumo

SANCHEZ INFANTE, Concepción; SERRANO SANCHEZ, Anixia; RAZON BEHAR, Roberto  e  REYES LOPEZ, Cristina. Pulmonary alveolar proteinosis. Rev Cubana Pediatr [online]. 2011, vol.83, n.4, pp. 413-422. ISSN 0034-7531.

The pulmonary alveolar proteinosis is a chronic respiratory disease characterized by surfactant metabolism alteration determining its abnormal accumulation in the alveolar space. It is a disease very rare and in literature only 500 cases have been reported; it was described for the first time in 1958. This is a case presentation of pulmonary alveolar proteinosis in an infant aged 2 months with energetic protein malnutrition admitted due to respiratory difficulty and hypoxemia and with radiologic images of the reticulonodulillary, in frosting glass, where initially is made the diagnosis of bronchopneumonia. In the face of unfavorable evolution and no response to treatment, a study was conducted to rule out chronic pulmonary diseases. Patient died confirming the diagnosis according to the pathologic anatomy. A review on subject is carried out.

Palavras-chave : pulmonary alveolar proteinosis; PAP; bronchopneumonia.

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