Meu SciELO
Serviços Personalizados
Artigo
Indicadores
- Citado por SciELO
Links relacionados
- Similares em SciELO
Compartilhar
Revista Cubana de Pediatría
versão On-line ISSN 1561-3119
Resumo
NARANJO UGALDE, Alfredo Mario; FLEITAS RUISANCHEZ, Elsa e AGUILERA SANCHEZ, Eutivides. A decade of care to patients with hypertrophic cardiomyopathy. Rev Cubana Pediatr [online]. 2021, vol.93, n.3 Epub 01-Out-2021. ISSN 1561-3119.
introduction:
Hypertrophic cardiomyopathy is a disease derived from autosomal dominant genetic alteration that causes an increase in the mass of the left ventricle, and can be obstructive or not. It is the leading cause of sudden death in young adults.
Objective:
Show the prevalence of hypertrophic cardiomyopathy and its forms of presentation in the practice of the "William Soler" Pediatric Cardiocenter.
Methods:
Retrospective, observational, longitudinal study of a case series. Demographic and clinical variables were summarized in the admissions made during 10 years of patients diagnosed with hypertrophic cardiomyopathy whom were analyzed as appropriate with qualitative and quantitative variable testing.
Results:
21 patients were identified; 12 with obstructive characteristics and 9 with non-obstructive ones. There was no predominance of sex. The average diagnostic age and clinical onset of patients with obstructive disease was significantly lower than the ages of patients without obstruction of the left outflow tract. Diagnosis was possible in more than 50% of cases by suspicion due to a murmur or by investigation. Surgical treatment allowed a significant reduction in the gradient of the left outflow tract. Propranolol was the most widely used beta-blocker according to international consensus. There were no deaths in the series studied.
Conclusions:
Hypertrophic cardiomyopathy has a low prevalence in cardiopediatric practice. Early symptoms correspond to the obstructive variety. Early diagnosis and specific treatment ensure better quality and life expectancy for carriers of this condition.
Palavras-chave : Hypertrophic cardiomyopathy; sudden death.