SciELO - Scientific Electronic Library Online

vol.59 número4Necrolisis tóxica epidérmica en cuidados intensivos índice de autoresíndice de assuntospesquisa de artigos
Home Pagelista alfabética de periódicos  

Serviços Personalizados



  • Não possue artigos citadosCitado por SciELO

Links relacionados

  • Não possue artigos similaresSimilares em SciELO


Revista Cubana de Medicina

versão On-line ISSN 1561-302X


PINO ALFONSO, Pedro Pablo  e  HERNANDEZ MORENO, Laura. Pulmonary lymphangioleiomyomatosis. Rev cubana med [online]. 2020, vol.59, n.4  Epub 15-Nov-2020. ISSN 1561-302X.


Pulmonary lymphangioleiomyomatosis constitutes a challenge, both in its diagnostic management and in the care of complications. It is a rare disease characterized by the proliferation of smooth muscle around the bronchovascular and lymphatic structures and in the pulmonary interstitium, together with cystic dilation of the terminal air spaces.


To describe a diagnosed case of pulmonary lymphangioleiomyomatosis.

Case report:

A case of pulmonary lymphangioleiomyomatosis is reported, which was clinically showed as recurrent pneumothorax. A definitive diagnosis was reached by performing a lung biopsy.


Lymphangioleiomyomatosis is a rare entity that mainly affects women of childbearing age and is characterized by the presence of a diffuse cystic pattern. Its prevalence and incidence is unknown.


It can be concluded that the presence of spontaneous or recurrent pneumothorax in a woman of childbearing age, or pregnant, should be suspected lymphangioleiomyomatosis.

Palavras-chave : lymphangioleiomyomatosis; lung tumor; pneumothorax.

        · resumo em Espanhol     · texto em Espanhol     · Espanhol ( pdf )