SciELO - Scientific Electronic Library Online

vol.60 suppl.1Cardiotoxicidad inducida por trastuzumab en paciente con carcinoma de mama HER-2 positivoSíndrome de Evans Fisher índice de autoresíndice de assuntospesquisa de artigos
Home Pagelista alfabética de periódicos  

Serviços Personalizados




  • Não possue artigos citadosCitado por SciELO

Links relacionados

  • Não possue artigos similaresSimilares em SciELO


Revista Cubana de Medicina

versão impressa ISSN 0034-7523versão On-line ISSN 1561-302X


HERNANDEZ PERERA, Julio César; VALDES SEDENO, Raúl Roberto; SABATIER, Carlos Alfonso  e  PINEIRO PEREZ, Dania. Sporadic inclusion body myositis. Rev cubana med [online]. 2021, vol.60, suppl.1, e1843.  Epub 01-Dez-2021. ISSN 0034-7523.

Despite being the most common primary myopathy in men over 50 years of age, sporadic inclusion body myositis (ICM) is a rare disease. On many occasions its diagnosis is delayed, which is why the importance of an adequate clinical assessment and timely indication of complementary studies is reinforced. This article reports a case that has the peculiarity of affecting a mestizo patient, with no established involvement in the deep flexors of his hands and with elements of severity, determined by the presence of high functional dysphagia and dyspnea in the supine position. There have not been publication reports on this disease in Cuba. Clinically, the condition is characterized by combined distal and proximal muscle weakness, electromyography (EMG) with mixed neuropathic and myopathic impairment, and poor response to immunosuppressive therapy. Muscle biopsy helps establish the definitive diagnosis by demonstrating the presence of distinctive inclusions in the muscle fibers. The prognosis is bleak, showing progressive behavior affecting quality of life and leading to advanced physical disability.

Palavras-chave : inclusion body myositis; myositis; rare diseases; electromyography; swallowing disorder.

        · resumo em Espanhol     · texto em Espanhol     · Espanhol ( pdf )