Resumen

MARTI CASTELLO, Eloísa et al. Manifestaciones digestivas en pacientes con fibrosis quística. Rev Cubana Pediatr [online]. 1996, vol.68, n.2, pp.125-130. ISSN 0034-7531.

Most of the patients suffering from cystic fibrosis present an exocrine insufficiency of the pancreatic function leading to complex digestive disorders. 8 patients between 1 and 12 years old with the diagnosis of cystic fibrosis are studied. Pancreatic enzymes in serum, protein electrophoresis, and viral markers of hepatitis B and C were carried out. Abdominal ultrasound, esophageal, hepatic and biliary gammagraphy were also performed. The most frequent clinical manifestations were steatorrhea, abdominal colics and hepatomegalia. Augmented lipase in serum was found in two patients with pancreatic sufficiency, whereas transaminases were normal in all of them. 3 patients showed clinical manifestations and 2 had gastroesophageal reflux and rectal prolapse, respectively. It was observed that with the therapeutic control of these manifestations a good nutrional status and a better quality of life are reported.

Palabras clave : CYSTIC FIBROSIS [complications]; LIVER [enzymology]; PANCREAS [enzymology]; AMY-LASES [blood]; LIPASE [blood]; ELECTROPHORESIS; IONTOPHORESIS, ELECTROPHORESIS SWEATING..