Abstract

LLANES CESPEDES, Ruperto; RODRIGUEZ FERNANDEZ, Ana Luisa; GONZALEZ FERNANDEZ, Sara Idalia  and  LOPEZ DELGADO, Felipe Rolando. Enfisema lobar congénito: Experiencia con 15 casos. Rev Cubana Pediatr [online]. 2003, vol.75, n.4. ISSN 0034-7531.

The congenital lobar emphysema is a congenital cystic malformation of the lung mostly seen in children. A retrospective study was conducted among 15 patients treated at "William Soler" Pediatric Teaching Hospital for 10 years aimed at studying the clinical and therapeutical behavior. It was found that 10 cases were females (66.66 %) and 5 were males (33.33 %). The age at the onset of the symptoms ranged from 24 hours to 24 weeks. The most frequent clinical manifestation was dyspnea in 14 patients (93.33 %). The left upper lobule was more severely affected in 9 cases (60.00 %), followed by the right medial lobule in 5 children (33.33 %) and the upper right lobule in 1 (6.66 %). Lobectomy was performed in most of the cases. It was concluded that this disease was more common in females under 24 weeks and in the left upper lobule. The severity of the clinical picture led to emergency surgery in many patients.

Keywords : PULMONARY EMPHYSEMA [congenital]; CYSTIC ADENOMATOID MALFORMATION OF LUNG, CONGENITAL [surgery]; INFANT NEWBORN DISEASES; PNEUMONECTOMY.