Revista Cubana de Pediatría
versión On-line ISSN 1561-3119
POZO ALONSO, Albia J. et al. Landau-Kleffner's syndrome: Reports of two casesLandau-Kleffner's syndrome. Rev Cubana Pediatr [online]. 2005, vol.77, n.2, pp. 0-0. ISSN 1561-3119.
Two children with the clinical and electroencephalographic criteria of Landau-Kleffner's syndrome are presented. In one of the patients, the difficulties for understanding the language and for the spontaneous oral expression started at 6 years old. In the other case, they were manifested at 6 years and 9 months old. One of the children has not had epileptic seizures so far. In this patient, the single positron emission computerized tomography (brain SPECT) showed a mild bilateral posterior temporoparietal hypoperfusion. The epileptic seizures in the other child started when he was 2 years and 6 months old and were focal , simple, motor and secondarily generalized. He has not had seizures for a year. Both patients had a favorable response to prednisone from the clinical and electroencephalographic point of view. The difficulties for understanding and oral expression persist in a child, although he has improved. It is concluded that the existence of an acquired aphasia and the discharges observed in the electroencephalogram are very important for the diagnosis of this syndrome
Palabras llave : Acquired epileptic aphasia; verbal auditive agnosia; epileptic encephalopathy; Landau-Kleffner's syndrome.