Resumen

HERNANDEZ BAGUER, Raisa et al. Clinical characteristics and evolution of retinosis pigmentosa in adolescents. Rev Cubana Pediatr [online]. 2008, vol.80, n.2. ISSN 0034-7531.

INTRODUCTION. Retinosis pigmentosa is the most frequent cause of retina dystrophy. Ocular diseases of dystrophic type, genetic origin and progressive course appear in adolescence. The objective of the present study is to identify the clinical characteristics and evolution of retinosis pigmentosa in adolescence. METHOD. A descriptive and prospective study was conducted among young subjects aged 10-14 (group 1) and 15-19 (group II) of both sexes that were seen at the National Pediatric Centre of Retinosis between 2002 and 2006. Heredity, symptoms, age, time elapsed; general diseases and electroretinogram were observed. The transparent means, fundus oculi, biomicroscopy and perimetry were performed at the beginning, at a year and at the end of the study. Taking into consideration the acuity and visual field, the cases were classified into 4 stages. RESULTS. White males prevailed. Opacities of the crystalline were found in 61 eyes (71.4 %), mainly in group 2. At the end of the study, 32 adolescents (76.2 %) had no progressive evolution; 5 (11.9 %), fairly progressive; and 5 (11.9 %), very progressive, with a marked worsening of the visual function. CONCLUSIONS. The characteristics of retinosis pigementosa identified in most of the youth agreed with the first stages of the disease. The evolution has not been progressive in most of the adolescents of both groups, which makes us think that the biological changes of this stage of life do not apparently worsen the course of the ocular disease.

Palabras clave : Retinosis pigmentosa; adolescence; night blindness; retinal dystrophy.

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