Revista Cubana de Pediatría
On-line version ISSN 1561-3119
POZO ALONSO, Albia et al. Hyperpotassemia periodic paralysis. Rev Cubana Pediatr [online]. 2011, vol.83, n.1, pp. 103-108. ISSN 1561-3119.
The periodic hyperpotassemia paralysis is a striated muscle channelopathy characterized by recurrent episodes of muscular asthenia that may to be triggered by exercise, cold, not rest after exercise and potassium support. This the case of a female patient aged 13 diagnosed with hyperpotassemia periodic paralysis without family backgrounds of this entity and also without associated myotonia. The seizures of muscular asthenia occurred almost daily and each 2 or 3 days with a variable length from a half hour to 24 to 48 hours. During a episode of muscular asthenia there were blood potassium concentrations of 7,14 mmol/L and the electromyogram showed a myopathic pattern. There was a frequency decrease of episodes of muscular asthenia at 2 months of treatment onset with oral acetazolamide.
Keywords : Muscular channelopathy; recurrent muscular asthenia; hyperpotassemia periodic paralysis.