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Revista Cubana de Pediatría

Print version ISSN 0034-7531


VARGAS DIAZ, José et al. Moyamoya disease, macrocephaly and intellectual impairment in an adolescent. Rev Cubana Pediatr [online]. 2013, vol.85, n.1, pp.112-119. ISSN 0034-7531.

The moyamoya pattern is characterized by chronic progressive narrowing of the terminal portion of the internal carotid artery or of its main terminal branches. Children suffering moyamoya disease regularly present with ischemic arterial ictus or transient ischemic strokes. Here is the case of an adolescent with intellectual impairment and macrocrania. The magnetic resonance imaging study of his brain showed repeated ischemic arterial infarctions and images suggestive of moyamoya disease, the pattern of which was later confirmed by digital subtraction angiography. The first objective was to intend to improve his cerebral irrigation by performing a revascularization surgery, but as long as this action was not accomplished, then taking aspirin as anti-platelet aggregation drug could prevent or reduce the risk of new cerebral infarctions or of repeated transient ischemic strokes.

Keywords : moyamoya syndrome; moyamoya disease; ischemic ictus in pediatrics; cerebrovascular disease in children.

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