Abstract

CESPEDES ALMIRA, Mariela; GONZALEZ MOREJON, Adel Eladio  and  SERRANO RICARDO, Giselle. Bland-White-Garland syndrome. Rev Cubana Pediatr [online]. 2016, vol.88, n.2. ISSN 0034-7531.

Bland-White-Garland syndrome is a rare but serious congenital defect since 90% of patients may die in the first year of life if they are not duly treated. From the period prior to the emergence of echocardiography up to the present day, the prevalence described in literature is 1 per 300 000 live births. Its clinical presentation is varied, and in spite of the fact that it is an anomaly of congenital origin, it does not only occur in pediatric ages. There are children suffering the adult variety of the syndrome; others who are masked under the clinical umbrella of other diseases or even children who are asymptomatic, so this syndrome can represent a serious health problem. Surgical treatment is the choice, with adequate prognosis and survival if diagnosis is made at early phase.

Keywords : Bland-White-Garland syndrome; congenital diseases.

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