Resumen

FUENTES RODRIGUEZ, Nelson; PRINCE LOPEZ, José Antonio  y  SALAS RUBIO, José Hernán. Klippel-Feil deformity with Arnold -Chiari type I malformation and syringomyelia. Rev Cub Med Mil [online]. 2005, vol.34, n.1. ISSN 0138-6557.

Klippel-Feil deformity is a developmental abnormality commonly affecting cervical vertebrae.The entity is generally associated with other deformities with or without abnormalities of the nervous system and of other organ systems. A case is reported of a 35-year-old adult patient without personal or family history of diseases causing deformities with osteal abnormalities or without them that was diagnosed Klippel-Feil disease with neural abnormalities by magnetic resonance imaging. As he clinically presented symptoms and signs characteristic of the medullocerebellar compression, craniotomy of the posterior fossa with laminectomy of C1 and duraplasty were performed. The evolution was satisfactory, and most of the symptoms disappeared.

Palabras clave : Klippel-Feil malformation; spinal-cervical abnormality; craniotomy of the posterior fossa; Arnold-Chiari malformation; rachidial- cervical malformation.