CRESPO GUERRA, Mario Carlos; LOPEZ DEL CASTILLO, Carlos Albornoz; AGUERO DIAZ, Álvaro    BASTIAN MANSO, Luis. Type 7 fissure of Tessier:  a case presentation. []. , 14, 5, pp. 0-0. ISSN 1025-0255.

Background: type 7 fissure of Tessier is a strange congenital deformity that may be presented with diverse degrees of severity; in a unilateral and incomplete most frequent way.  Objective: to report the first patient in Cuba with a bilateral type 7 fissure of Tessier of considerable severity. Clinical case: it is described a gemellary, female sex, white race patient; born on February 10th 2010 at the Maternal Hospital of Camagüey with a severe malformation of the face and a weight of 1784g. The neonatal clinical and pediatric history of the patient was reviewed as well as the most recent articles in on-line database dealt with the following topics: type 7 fissure of Tessier, transverse facial cleft and bilateral macrostomia.  Discussion: after the revision was found that have been reported until the year 2008 just 90 cases of bilateral congenital macrostomia and in our country it is not documented on this deformity. A patient diagnosed at the Maternal Hospital of Camagüey with a severe type 7 fissure of Tessier associated to a fissured soft palate and a hypoplasia with mandibular retrusion that dies to the 72 days of been born and some elements in her diagnosis and treatment to further cases are discussed. Conclusions: it is concluded that this is the first report in Cuba with a type 7 fissure of Tessier with such a severe magnitude.

: MACROSTOMIA; CONGENITAL ABNORMALITIES; CHILD; CASE STUDIES.

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