<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1028-4818</journal-id>
<journal-title><![CDATA[Multimed]]></journal-title>
<abbrev-journal-title><![CDATA[Multimed]]></abbrev-journal-title>
<issn>1028-4818</issn>
<publisher>
<publisher-name><![CDATA[Centro Provincial de Información de Ciencias Médicas]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1028-48182020000300680</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Osteocondromatosis múltiple. Caso clínico]]></article-title>
<article-title xml:lang="en"><![CDATA[Multiple osteochondromatosis. Clinical case]]></article-title>
<article-title xml:lang="pt"><![CDATA[Osteocondromatose múltipla. Caso clínico]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Guerrero Tamayo.]]></surname>
<given-names><![CDATA[Pavel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Garoz Fonseca.]]></surname>
<given-names><![CDATA[José Enrique]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Duany Almira.]]></surname>
<given-names><![CDATA[Luis Félix]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad de Ciencias Médicas de Granma Hospital Provincial Universitario Carlos Manuel de Céspedes ]]></institution>
<addr-line><![CDATA[Bayamo Granma]]></addr-line>
<country>Cuba</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>06</month>
<year>2020</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>06</month>
<year>2020</year>
</pub-date>
<volume>24</volume>
<numero>3</numero>
<fpage>680</fpage>
<lpage>689</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_arttext&amp;pid=S1028-48182020000300680&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_abstract&amp;pid=S1028-48182020000300680&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_pdf&amp;pid=S1028-48182020000300680&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN  Introducción: la osteocondromatosis múltiple hereditaria, entidad autosómica dominante, que se caracteriza por el crecimiento de múltiples tumores benignos llamados osteocondromas.  Presentación del caso: paciente femenina de 12 años de edad, que acude a consulta refiriendo dolor constante en rodilla derecha, más acentuado con la marcha. Examen físico SOMA: Aumento de volumen de rodilla derecha hacia sus caras externas e internas con dolor a la palpación, se palpa masa dura, no movible, de bordes irregulares. También se constatan tumoraciones de similares características en ambos hombros y rodillas.  Discusión: se le realizan radiografías, observando lesiones óseas en la metáfisis proximal de ambos húmeros a predominio derecho. Exostosis a nivel de metáfisis proximal y distal de ambos fémures, en tibia y peroné bilateral. En rodilla derecha se observa crecimiento hacia la línea media de la tumoración del peroné desplazando en valgo la metáfisis proximal de la tibia.  Conclusiones: se plantea una exostosis múltiple como diagnóstico. Se realizó tratamiento quirúrgico escisión tumoral del extremo proximal del peroné de la rodilla derecha y de la cara interna de la metáfisis proximal de la tibia y biopsia que confirmó el diagnóstico.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT  Introduction: hereditary multiple osteochondromatosis, an autosomal dominant entity, characterized by the growth of multiple benign tumors called osteochondromas.  Case presentation:  12-year-old female patient, who comes to the consultation referring to constant pain in the right knee, more accentuated with the gait. PHYSICAL exam SOMA: Increase of volume of right knee towards their outer and inner faces with pain to palpation, it palps hard mass, not movable, of irregular edges. Tumors of similar characteristics are also found in both shoulders and knees.  Discussion:  X-rays are performed, observing bone lesions in the proximal metaphysis of both humeruses to right predominance. Exostosis at the level of proximal and distal metaphysis of both femurs, in tibia and bilateral fibula. In the right knee, growth is observed towards the midline of the fibula tumor displacing the proximal metaphysis of the tibia in valgo.  Conclusions:  Multiple exostosis is raised as a diagnosis. Surgical treatment was performed tumor excision of the proximal end of the fibula of the right knee and the inner face of the proximal metaphysis of the tibia and biopsy that confirmed the diagnosis.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[RESUMO  Introdução: osteocondromatose múltipla hereditária, uma entidade autossômica dominante, caracterizada pelo crescimento de múltiplos tumores benignos chamados osteochondromas.  Apresentação do caso:  paciente do sexo feminino de 12 anos, que chega à consulta referindo-se a dores constantes no joelho direito, mais acentuadas com a marcha. Exame FÍSICO SOMA: Aumento do volume do joelho direito em direção aos seus rostos externos e internos com dor à palpação, palpa massa dura, não móvel, de bordas irregulares. Tumores de características semelhantes também são encontrados em ambos os ombros e joelhos.  Discussão:  São realizados raios-X, observando lesões ósseas na metafise proximal de ambos os úmeros à predominância direita. Exostose ao nível de metafísica proximal e distal de ambos os fêmures, natíbia e fíbula bilateral. No joelho direito, observa-se crescimento para a linha média do tumor de fíbula deslocando a metafísica proximal da tíbia em valgo.  Conclusões:  A exostose múltipla é levantada como diagnóstico. Foi realizado tratamento cirúrgico excisão tumoral da extremidade proximal da fíbula do joelho direito e da face interna da metafise proximal da tíbia e biópsia que confirmou o diagnóstico.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Exostosis]]></kwd>
<kwd lng="es"><![CDATA[Osteocondromatosis]]></kwd>
<kwd lng="es"><![CDATA[Exostosis múltiple hereditaria]]></kwd>
<kwd lng="es"><![CDATA[Imagen por resonancia magnética]]></kwd>
<kwd lng="es"><![CDATA[Radiografía digital]]></kwd>
<kwd lng="en"><![CDATA[Exostosis]]></kwd>
<kwd lng="en"><![CDATA[Osteochondromatosis]]></kwd>
<kwd lng="en"><![CDATA[Hereditary multiple exostosis]]></kwd>
<kwd lng="en"><![CDATA[Magnetic resonance imaging]]></kwd>
<kwd lng="en"><![CDATA[Digital radiography]]></kwd>
<kwd lng="pt"><![CDATA[Exostose]]></kwd>
<kwd lng="pt"><![CDATA[Osteocondromatose]]></kwd>
<kwd lng="pt"><![CDATA[Exostose múltipla hereditária]]></kwd>
<kwd lng="pt"><![CDATA[Imagem de ressonância magnética]]></kwd>
<kwd lng="pt"><![CDATA[Radiografia digital]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<label>1</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Santos Guzmán]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Cantú Reyna]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
<name>
<surname><![CDATA[Cano Muñoz]]></surname>
<given-names><![CDATA[AL]]></given-names>
</name>
<name>
<surname><![CDATA[Pulido Ayala]]></surname>
<given-names><![CDATA[AK]]></given-names>
</name>
<name>
<surname><![CDATA[García]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Osteocondromatosis múltiple hereditaria en una familia]]></article-title>
<source><![CDATA[Bol Med Hosp Infant Mex]]></source>
<year>2016</year>
<volume>73</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>111-6</page-range></nlm-citation>
</ref>
<ref id="B2">
<label>2</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Stieber]]></surname>
<given-names><![CDATA[JR]]></given-names>
</name>
<name>
<surname><![CDATA[Dormans]]></surname>
<given-names><![CDATA[JP]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Manifestations of Hereditary Multiple Exostoses]]></article-title>
<source><![CDATA[J Am Acad Orthop Surg]]></source>
<year>2005</year>
<volume>13</volume>
<page-range>110-20</page-range></nlm-citation>
</ref>
<ref id="B3">
<label>3</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Orgaz Álvarez]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Lorente Jareño]]></surname>
<given-names><![CDATA[ML]]></given-names>
</name>
<name>
<surname><![CDATA[Gamero Medina]]></surname>
<given-names><![CDATA[V]]></given-names>
</name>
<name>
<surname><![CDATA[Cedeño Poveda]]></surname>
<given-names><![CDATA[MF]]></given-names>
</name>
<name>
<surname><![CDATA[Vara Cilla]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Bueno Sánchez]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Osteocondromatosis Múltiple Hereditaria Más allá del diagnóstico]]></article-title>
<source><![CDATA[SERAM]]></source>
<year>2014</year>
<volume>11</volume>
<numero>50</numero>
<issue>50</issue>
<page-range>1-39</page-range></nlm-citation>
</ref>
<ref id="B4">
<label>4</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Carpintero]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
<name>
<surname><![CDATA[del Fresno]]></surname>
<given-names><![CDATA[JA]]></given-names>
</name>
<name>
<surname><![CDATA[Carpintero]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Gálvez]]></surname>
<given-names><![CDATA[MJ]]></given-names>
</name>
<name>
<surname><![CDATA[Marín]]></surname>
<given-names><![CDATA[MA]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Complicaciones de los Osteocondromas]]></article-title>
<source><![CDATA[Rev Española de Cirugía Osteoarticular]]></source>
<year>2009</year>
<volume>237</volume>
<numero>44</numero>
<issue>44</issue>
<page-range>22-9</page-range></nlm-citation>
</ref>
<ref id="B5">
<label>5</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Wells]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Birchard]]></surname>
<given-names><![CDATA[Z]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[A 40-Year-Old Male Presenting with Hereditary Multiple Exostosis: Management and Considerations]]></article-title>
<source><![CDATA[Hindawi]]></source>
<year>2019</year>
</nlm-citation>
</ref>
<ref id="B6">
<label>6</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Mederos Mesa]]></surname>
<given-names><![CDATA[LR]]></given-names>
</name>
<name>
<surname><![CDATA[Ginorio Suárez]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
<name>
<surname><![CDATA[Pineda Folgoso]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Exostosis múltiple hereditaria]]></article-title>
<source><![CDATA[MediCiego]]></source>
<year>2018</year>
<volume>24</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>22-7</page-range></nlm-citation>
</ref>
<ref id="B7">
<label>7</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Eke]]></surname>
<given-names><![CDATA[GK]]></given-names>
</name>
<name>
<surname><![CDATA[Omunakwe]]></surname>
<given-names><![CDATA[HE]]></given-names>
</name>
<name>
<surname><![CDATA[Echem]]></surname>
<given-names><![CDATA[RC]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Hereditary multiple exostoses in a15-year-old boy A case report and review of literature. Case Report]]></article-title>
<source><![CDATA[Niger J Paediatr]]></source>
<year>2016</year>
<volume>43</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>295-8</page-range></nlm-citation>
</ref>
<ref id="B8">
<label>8</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Sáez Moreno]]></surname>
<given-names><![CDATA[MA]]></given-names>
</name>
<name>
<surname><![CDATA[Torres Hidalgo]]></surname>
<given-names><![CDATA[JL]]></given-names>
</name>
<name>
<surname><![CDATA[González González]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Manejo de lesiones óseas osteocodroma]]></article-title>
<source><![CDATA[Rev Clin Med Fam]]></source>
<year>2017</year>
<volume>10</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>154-7</page-range></nlm-citation>
</ref>
<ref id="B9">
<label>9</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Akbaroghli]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Balali]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Kamalidehghan]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
<name>
<surname><![CDATA[Saber]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Aryani]]></surname>
<given-names><![CDATA[O]]></given-names>
</name>
<name>
<surname><![CDATA[Yong Meng]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Identification of a new mutation in an Iranian family with hereditary multiple osteochondromas]]></article-title>
<source><![CDATA[Ther Clin Risk Manag]]></source>
<year>2016</year>
<volume>13</volume>
<page-range>15-9</page-range></nlm-citation>
</ref>
<ref id="B10">
<label>10</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Cammarata Scalisi]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
<name>
<surname><![CDATA[Stock]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
<name>
<surname><![CDATA[Avendaño]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Cozar]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Balcells]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Grinberg]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Estudio clínico y molecular en una familia con osteocondromatosis múltiple]]></article-title>
<source><![CDATA[Acta Ortop Mex]]></source>
<year>2018</year>
<volume>32</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>108-11</page-range></nlm-citation>
</ref>
<ref id="B11">
<label>11</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Aedo Martín]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Martínez Álvarez]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Vara Patudo]]></surname>
<given-names><![CDATA[I]]></given-names>
</name>
<name>
<surname><![CDATA[Alonso Hernández]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Fusión radiocubital en paciente con osteocondromatosis múltiple hereditaria]]></article-title>
<source><![CDATA[Revista Iberoamericana de Cirugía de la Mano]]></source>
<year>2017</year>
<volume>45</volume>
<page-range>40-4</page-range></nlm-citation>
</ref>
<ref id="B12">
<label>12</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Saint Pierre Contreras]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Bravo Rius]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
<name>
<surname><![CDATA[Valencia Castillo]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Conei Valencia]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Osteocondroma como hallazgo incidental en Úlcera Varicosa Sobreinfectada en miembro inferior]]></article-title>
<source><![CDATA[J Health Med SCI]]></source>
<year>2018</year>
<volume>4</volume>
<page-range>5-9</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
