<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0034-7531</journal-id>
<journal-title><![CDATA[Revista Cubana de Pediatría]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Cubana Pediatr]]></abbrev-journal-title>
<issn>0034-7531</issn>
<publisher>
<publisher-name><![CDATA[Centro Nacional de Información de Ciencias MédicasEditorial Ciencias Médicas]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0034-75312022000100014</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Presentación inusual del adenoma pleomorfo congénito de fosa nasal en neonato]]></article-title>
<article-title xml:lang="en"><![CDATA[Unusual presentation of congenital pleomorphic adenoma of the nostril in a newborn]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rodríguez López]]></surname>
<given-names><![CDATA[Yamisel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Quintero Noa]]></surname>
<given-names><![CDATA[Julianis Loraine]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Mares Villaseñor]]></surname>
<given-names><![CDATA[Norma Andrea]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Hernández-Cordero]]></surname>
<given-names><![CDATA[María del Carmen]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Pediátrico Docente Universitario William Soler Ledea Departamento de Otorrinolaringología ]]></institution>
<addr-line><![CDATA[ La Habana]]></addr-line>
<country>Cuba</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Hospital Pediátrico Docente Universitario William Soler Ledea Departamento de Otorrinolaringología Departamento Docencia-Investigación]]></institution>
<addr-line><![CDATA[ La Habana]]></addr-line>
<country>Cuba</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Hospital Clínico Quirúrgico Joaquín Albarrán Departamento de Otorrinolaringología ]]></institution>
<addr-line><![CDATA[ La Habana]]></addr-line>
<country>Cuba</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,Centro de Neurociencias de Cuba  ]]></institution>
<addr-line><![CDATA[ La Habana]]></addr-line>
<country>Cuba</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>03</month>
<year>2022</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>03</month>
<year>2022</year>
</pub-date>
<volume>94</volume>
<numero>1</numero>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_arttext&amp;pid=S0034-75312022000100014&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_abstract&amp;pid=S0034-75312022000100014&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_pdf&amp;pid=S0034-75312022000100014&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN  Introducción:  El adenoma pleomorfo es la neoplasia benigna más frecuente en las glándulas salivales, su localización en vías aéreas superiores es poco frecuente.  Objetivo: Describir la inusual presentación de un adenoma pleomorfo congénito nasal, no descrito con anterioridad en Cuba.  Presentación del caso: se presenta un caso raro de recién nacido con datos clínicos de obstrucción nasal horas después de su nacimiento. Previos estudios y resultado de biopsia del tumor intranasal determinaron adenoma pleomorfo congénito. Se realizó exéresis de tumor por cirugía endoscópica nasal.  Conclusiones: El adenoma pleomorfo debe ser considerado un diagnóstico diferencial en todas las edades; sospechar ante un paciente con síntomas de obstrucción unilateral o epistaxis. Un diagnóstico temprano permite un tratamiento oportuno con abordaje quirúrgico endoscópico menos invasivo y una menor tasa de recidiva. Este tumor se destaca por su potencial recurrencia o transformación maligna por lo que es importante mantener vigilancia endoscópica e imagenológica.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT  Introduction:  Pleomorphic adenoma is the most frequent benign neoplasm in the salivary glands; its location in the upper airways is rare.  Objective:  Describe the unusual presentation of a nasal congenital pleomorphic adenoma, not previously described in Cuba.  Case Presentation:  A rare case of a newborn with clinical data of nasal obstruction hours after birth is presented. Previous studies and biopsy result of the intranasal tumor determined congenital pleomorphic adenoma. Tumor excision was performed by endoscopic nasal surgery.  Conclusions:  Pleomorphic adenoma should be considered a differential diagnosis at all ages. Suspecting should be normal when a patient has symptoms of unilateral obstruction or epistaxis. Early diagnosis allows timely treatment with a less invasive endoscopic surgical approach and a lower rate of recurrence. This tumor stands out for its potential recurrence or malignant transformation, so it is important to maintain endoscopic and imaging surveillance.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[adenoma pleomorfo congénito]]></kwd>
<kwd lng="es"><![CDATA[tabique nasal]]></kwd>
<kwd lng="es"><![CDATA[cirugía endoscópica]]></kwd>
<kwd lng="en"><![CDATA[congenital pleomorphic adenoma]]></kwd>
<kwd lng="en"><![CDATA[nasal septum]]></kwd>
<kwd lng="en"><![CDATA[endoscopic surgery]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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