<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1608-8921</journal-id>
<journal-title><![CDATA[Gaceta Médica Espirituana]]></journal-title>
<abbrev-journal-title><![CDATA[Gac Méd Espirit]]></abbrev-journal-title>
<issn>1608-8921</issn>
<publisher>
<publisher-name><![CDATA[Universidad de Ciencias Médicas de Sancti Spíritus]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1608-89212020000200042</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Caracterización clínico-epidemiológica en pacientes discapacitados visuales por retinosis pigmentaria. Sancti Spíritus. 2009-2019]]></article-title>
<article-title xml:lang="en"><![CDATA[Clinical and epidemiological characterization in visual impaired patients due to retinitis pigmentosa. Sancti Spíritus. 2009-2019]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rodríguez Montero]]></surname>
<given-names><![CDATA[Pedra]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Toledo Rodríguez]]></surname>
<given-names><![CDATA[Yunia]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Pina García]]></surname>
<given-names><![CDATA[Maritza]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Álvarez Martínez]]></surname>
<given-names><![CDATA[Yeneisy]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[León Bernal]]></surname>
<given-names><![CDATA[Danysleidi]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Provincial General Camilo Cienfuegos  ]]></institution>
<addr-line><![CDATA[Sancti Spíritus ]]></addr-line>
<country>Cuba</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>08</month>
<year>2020</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>08</month>
<year>2020</year>
</pub-date>
<volume>22</volume>
<numero>2</numero>
<fpage>42</fpage>
<lpage>50</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_arttext&amp;pid=S1608-89212020000200042&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_abstract&amp;pid=S1608-89212020000200042&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_pdf&amp;pid=S1608-89212020000200042&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN  Fundamento:  La retinosis pigmentaria constituye una causa de discapacidad visual que provoca alteraciones psicológicas y sociales al paciente.  Objetivo:  Describir las características clínicas y epidemiológicas en pacientes discapacitados visuales por retinosis pigmentaria de la provincia Sancti Spíritus.  Metodología:  Se realizó un estudio descriptivo, que incluyó 140 pacientes discapacitados visuales afectados por retinosis pigmentaria.  Resultados: El grupo etario entre los 29 y 56 años fue el más afectado (78.1 %), el 65 % era del sexo masculino, predominó el color blanco de la piel (87.1 %), sobresalió la catarata como la afección ocular (13.6 %), el 16.4 % presentó hipertensión arterial; la mayoría de los discapacitados no presentó hábitos tóxicos (55 %), prevaleció el debut precoz en el 70 % de los casos. La forma típica de la enfermedad se observó en el 98.5 % de los enfermos, el 67 % manifestó un estadio clínico de la enfermedad grado IV, así como la herencia autosómica recesiva en el 36.4 %.  Conclusiones:  Predominio de los enfermos en los grupos etario entre 29 y 56 años, masculino, color blanco de la piel; la catarata como patología ocular más frecuente junto a la hipertensión arterial dentro las enfermedades sistémicas; la mayoría de los discapacitados no presentó hábitos tóxicos. El debut precoz, la forma típica, el estadio IV de la enfermedad, así como la herencia autosómica dominante prevalecieron en el estudio.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT  Background:  Retinitis pigmentosa is a cause of visual impairment that causes psychological and social alterations to the patient.  Objective:  To describe the clinical and epidemiological characteristics in visual impaired patients due to retinitis pigmentosa in Sancti Spíritus province.  Methodology:  A descriptive study was carried out, which included 140 visual impaired patients affected by retinitis pigmentosa.  Results:  The age group between 29 and 56 years old was the most affected (78.1 %), 65 % were male, white skin predominated (87.1 %), cataract stood out as an eye condition (13.6 %), 16.4 % presented arterial hypertension; most of the disabled did not present toxic habits (55 %), early debut prevailed in 70 % of cases. The typical form of the disease was observed in 98.5 % of patients, 67 % showed a clinical stage of grade IV disease, as well as autosomal recessive inheritance in 36.4 %.  Conclusions:  Prevalence of patients in the age groups between 29 and 56 years, male, white skin color; cataract as the most frequent ocular pathology together with arterial hypertension within systemic diseases; the majority of the disabled patients did not show toxic habits. Early debut, typical form, stage IV disease, and autosomal dominant inheritance prevailed in the study.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Discapacitados visuales]]></kwd>
<kwd lng="es"><![CDATA[personas con daño visual]]></kwd>
<kwd lng="es"><![CDATA[retinitis pigmentosa]]></kwd>
<kwd lng="es"><![CDATA[retinosis pigmentaria]]></kwd>
<kwd lng="es"><![CDATA[herencia]]></kwd>
<kwd lng="es"><![CDATA[patrón de herencia]]></kwd>
<kwd lng="es"><![CDATA[estadio]]></kwd>
<kwd lng="es"><![CDATA[debut]]></kwd>
<kwd lng="es"><![CDATA[hábitos tóxicos]]></kwd>
<kwd lng="en"><![CDATA[Visual impaired patients]]></kwd>
<kwd lng="en"><![CDATA[visually impaired persons]]></kwd>
<kwd lng="en"><![CDATA[retinitis pigmentosa]]></kwd>
<kwd lng="en"><![CDATA[inheritance]]></kwd>
<kwd lng="en"><![CDATA[inheritance patterns]]></kwd>
<kwd lng="en"><![CDATA[stage]]></kwd>
<kwd lng="en"><![CDATA[debut]]></kwd>
<kwd lng="en"><![CDATA[toxic habits]]></kwd>
</kwd-group>
</article-meta>
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