<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0034-7531</journal-id>
<journal-title><![CDATA[Revista Cubana de Pediatría]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Cubana Pediatr]]></abbrev-journal-title>
<issn>0034-7531</issn>
<publisher>
<publisher-name><![CDATA[Centro Nacional de Información de Ciencias MédicasEditorial Ciencias Médicas]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0034-75312020000100011</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Seudo síndrome prune belly]]></article-title>
<article-title xml:lang="en"><![CDATA[Pseudo Prune-belly syndrome]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Durán Álvarez]]></surname>
<given-names><![CDATA[Sandalio]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Pediátrico Universitario &#8220;William Soler&#8221;  ]]></institution>
<addr-line><![CDATA[La Habana ]]></addr-line>
<country>Cuba</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>03</month>
<year>2020</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>03</month>
<year>2020</year>
</pub-date>
<volume>92</volume>
<numero>1</numero>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_arttext&amp;pid=S0034-75312020000100011&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_abstract&amp;pid=S0034-75312020000100011&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_pdf&amp;pid=S0034-75312020000100011&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN  Introducción:  El síndrome prune belly es una rara y compleja anomalía congénita y el seudo prune belly es aún más raro y en muchas ocasiones no se diagnostica como tal.  Objetivo:  Describir un paciente con las características de este síndrome.  Presentación del caso:  Feto de sexo masculino que en la semana 23 del embarazo el ultrasonido prenatal detectó dilatación pélvica bilateral y se propuso la interrupción del embarazo que no fue aceptada por los padres. Al nacer se observa criptorquidia bilateral, el ultrasonido renal a las 34 horas de nacido confirma dilatación pélvica bilateral severa, se indica profilaxis con cefalexina, y a los cuatro dias de nacido es enviado a consulta de nefrología. Al llegar a consulta se observa la ausencia de testículos en ambas bolsas escrotales y el ultrasonido abdominal a los 16 dias confirma dilatación pélvica renal derecha severa y uréter dilatado en su tercio superior con 6 mm de diámetro y ureteropielocaliectasia severa del lado izquierdo; no se visualiza testículo derecho y el izquierdo en canal inguinal mide 7 × 10 mm. La gammagrafía estática demostró hipocaptación marcada del radiofármaco por el riñón izquierdo y disminución de la función renal relativa y en la uretrocistografía miccional se encontró dilatación vesical y reflujo vesicoureteral con ureterohidronefrosis bilateral.  Conclusiones:  El seudo síndrome prune belly presenta alteraciones complejas del tracto urinario que son las que establecen el pronóstico en estos casos.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT  Introduction:  Prune belly syndrome is a rare and complex congenital anomaly and the pseudo prune belly is even rarer and often not diagnosed as such.  Objective:  To describe a patient with the characteristics of this syndrome.  Presentation of the case:  Male fetus that in the 23rd week of pregnancy it was detected a bilateral pelvic dilatation in the prenatal ultrasound; and it was proposed the termination of pregnancy which was not accepted by the parents. At birth it is observed bilateral cryptorchidism; the renal ultrasound at 34 hours after birth confirmed bilateral severe pelvic dilation, it is indicated prophylaxis with cephalexin, and at four days after birth, the newborn is remitted to the Nephrology consultation. In the consultation it was noticed the absence of scrotal sacs in both testicles and the abdominal ultrasound at 16 days after birth confirmed severe right renal pelvic dilatation and dilated ureter in its upper third with 6 mm of diameter and severe uretero-pielocaliectasy in the left side; it is not visualized the right testicle and the left in the inguinal channel measured 7 × 10 mm. Static scintigraphy showed marked hypocaptation of the radiopharmaceutical by the left kidney and decreased relative renal function, and in the voiding cystourethrogram it was found bladder dilation and vesicoureteral reflux with bilateral ureterohydronephrosis.  Conclusions:  The pseudo prune belly syndrome presents complex abnormalities of the urinary tract that are those which establish the prognosis in these cases.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[síndrome prune belly]]></kwd>
<kwd lng="es"><![CDATA[seudo síndrome prune belly]]></kwd>
<kwd lng="es"><![CDATA[seudo seudo síndrome prune belly]]></kwd>
<kwd lng="en"><![CDATA[Prune belly Syndrome]]></kwd>
<kwd lng="en"><![CDATA[Prune belly pseudo-syndrome]]></kwd>
<kwd lng="en"><![CDATA[Prune belly seudosuedo-syndrome]]></kwd>
</kwd-group>
</article-meta>
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