<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0034-7531</journal-id>
<journal-title><![CDATA[Revista Cubana de Pediatría]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Cubana Pediatr]]></abbrev-journal-title>
<issn>0034-7531</issn>
<publisher>
<publisher-name><![CDATA[Centro Nacional de Información de Ciencias MédicasEditorial Ciencias Médicas]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0034-75312021000100015</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Diagnóstico clínico de la incontinencia pigmentaria en dos neonatos con lesiones cutáneas vesículo-pustulosas]]></article-title>
<article-title xml:lang="en"><![CDATA[Clinical diagnosis of pigment incontinence in two neonates with vesicle-pustulous skin lesions]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Robaina Castellanos]]></surname>
<given-names><![CDATA[Gerardo Rogelio]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Sabido Toledo]]></surname>
<given-names><![CDATA[Lisbeth]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Riesgo Rodríguez]]></surname>
<given-names><![CDATA[Solangel de la Caridad]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Robaina Castellanos]]></surname>
<given-names><![CDATA[Martha Sonia]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Ginecoobstétrico Docente Provincial de Matanzas &#8220;José Ramón López Tabrane&#8221; Servicio de Neonatología ]]></institution>
<addr-line><![CDATA[Matanzas ]]></addr-line>
<country>Cuba</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Hospital Pediátrico Provincial de Matanzas &#8220;Eliseo Noel Caamaño&#8221; Servicio de Consulta externa ]]></institution>
<addr-line><![CDATA[Matanzas ]]></addr-line>
<country>Cuba</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Hospital Pediátrico Provincial de Matanzas &#8220;Eliseo Noel Caamaño&#8221; Departamento Docente ]]></institution>
<addr-line><![CDATA[Matanzas ]]></addr-line>
<country>Cuba</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,Instituto Nacional de Oncología y Radiolobiogía Servicio de Oncogenética ]]></institution>
<addr-line><![CDATA[La Habana ]]></addr-line>
<country>Cuba</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>03</month>
<year>2021</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>03</month>
<year>2021</year>
</pub-date>
<volume>93</volume>
<numero>1</numero>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_arttext&amp;pid=S0034-75312021000100015&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_abstract&amp;pid=S0034-75312021000100015&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_pdf&amp;pid=S0034-75312021000100015&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN  Introducción:  La incontinencia pigmentaria es un trastorno neuroectodérmico sistémico que en el recién nacido se diagnostica por la presencia de lesiones cutáneas de tipo eritemato-vesiculosas o vesículo-pustulosas, con distribución según las líneas de Blaschko, asociadas a eosinofilia en muestra de sangre.  Objetivo: Mostrar que es factible diagnosticar la incontinencia pigmentaria en el período neonatal, aún en casos esporádicos, mediante un adecuado ejercicio del método clínico.  Presentación de los casos: Se trata de dos recién nacidas femeninas, nacidas a término, con peso adecuado para la edad gestacional y sin antecedentes pre- y perinatales de interés; la primera de las cuales se presenta al tercer día de nacida con lesiones en piel, de aspecto vesículo-pustuloso, que seguían el recorrido del nervio ciático poplíteo externo. El segundo caso se presenta al 11no día de nacida con lesiones de tipo vesículo-ampulosas, en región externa de los cuatro miembros, con mejoría a los 26 días de vida. En ambos casos se plantea el diagnóstico de incontinencia pigmentaria esporádica.  Conclusiones: El diagnóstico de la incontinencia pigmentaria en el período neonatal constituye un reto, el cual es posible asumir si se lleva a cabo un adecuado uso del método clínico, con un minucioso diagnóstico diferencial. Para el diagnóstico, resulta útil establecer consenso a partir de un enfoque multidisciplinario.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT  Introduction:  Pigment incontinence is a systemic neuroectodermal disorder that in the newborn is diagnosed by the presence of skin lesions of erythematous-vesiculosus or vesicle-pustulous type, with distribution according to the Blaschko lines, associated with eosinophilia in the blood sample.  Objective:  Show that it is feasible to diagnose pigment incontinence in the neonatal period, even in sporadic cases, through proper performance of the clinical method.  Presentation of cases:  These are two female newborns, born full-term, with a suitable weight for gestational age and without a pre- and perinatal history of interest; the first case occurs on the third day of life, presenting skin lesions, vesicle-pustulous in appearance, which followed the path of the external popliteal sciatic nerve. The second case occurs on the 11th day of life with vesicle-ampulose lesions in the outer region of the four limbs, with improvement at 26 days of life. Diagnosis of sporadic pigment incontinence is stated in both cases.  Conclusions:  Diagnosing pigment incontinence in the neonatal period is a challenge, which can be assumed if proper use of the clinical method is carried out, with a thorough differential diagnosis.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[recién nacido]]></kwd>
<kwd lng="es"><![CDATA[diagnóstico]]></kwd>
<kwd lng="es"><![CDATA[genodermatosis]]></kwd>
<kwd lng="es"><![CDATA[incontinencia pigmentaria]]></kwd>
<kwd lng="es"><![CDATA[incontinentia pigmenti]]></kwd>
<kwd lng="es"><![CDATA[síndrome de Bloch-Sulzberger]]></kwd>
<kwd lng="en"><![CDATA[Newborn]]></kwd>
<kwd lng="en"><![CDATA[diagnosis]]></kwd>
<kwd lng="en"><![CDATA[genodermatosis]]></kwd>
<kwd lng="en"><![CDATA[pigment incontinence]]></kwd>
<kwd lng="en"><![CDATA[incontinentia pigmenti]]></kwd>
<kwd lng="en"><![CDATA[Bloch-Sulzberger syndrome]]></kwd>
</kwd-group>
</article-meta>
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