<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0138-600X</journal-id>
<journal-title><![CDATA[Revista Cubana de Obstetricia y Ginecología]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Cubana Obstet Ginecol]]></abbrev-journal-title>
<issn>0138-600X</issn>
<publisher>
<publisher-name><![CDATA[Editorial Ciencias Médicas]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0138-600X2019000400007</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Síndrome de Klippel Trenaunay Weber y embarazo]]></article-title>
<article-title xml:lang="en"><![CDATA[Klippel Trenaunay Weber Syndrome and Pregnancy]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Couret Cabrera]]></surname>
<given-names><![CDATA[Martha Patricia]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Sánchez Ramírez]]></surname>
<given-names><![CDATA[Niobys]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Ortúzar Chirino]]></surname>
<given-names><![CDATA[Ada Anisia]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Sanabria Arias]]></surname>
<given-names><![CDATA[Ana Mary]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Carrillo Bermúdez]]></surname>
<given-names><![CDATA[Lourdes]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Facultad de Medicina Manuel Fajardo Hospital Ginecobstétrico &#8220;Ramón González Coro&#8221; ]]></institution>
<addr-line><![CDATA[La Habana ]]></addr-line>
<country>Cuba</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2019</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2019</year>
</pub-date>
<volume>45</volume>
<numero>4</numero>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_arttext&amp;pid=S0138-600X2019000400007&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_abstract&amp;pid=S0138-600X2019000400007&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_pdf&amp;pid=S0138-600X2019000400007&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN  Introducción: El síndrome de Klippel Trenaunay Weber es una enfermedad vascular congénita, de causas desconocidas, caracterizada por hemangiomas planos, crecimiento excesivo de huesos y tejido blando, y venas varicosas. Cuando se asocia al embarazo incrementa la morbilidad y mortalidad materna y fetal.  Objetivo:  Describir dos casos clínicos de gestantes con este síndrome las cuales fueron atendidas en el Hospital Ginecobstétrico Docente &#8220;Ramón González Coro&#8221; en La Habana, Cuba.  Métodos: Estudio descriptivo, retrospectivo, de dos casos mediante técnica de recolección de información, análisis de la historia clínica y búsqueda de literatura actualizada. El mismo se efectuó conforme a las reglamentaciones y principios éticos existentes para la investigación en humanos. No fue necesario que las pacientes ofrecieran su consentimiento informado.  Presentación de casos: Los dos casos presentados fueron gestantes adolescentes a las cuales se les dio seguimiento en consulta multidisciplinaria y se les realizó cesárea a las 38 semanas, la primera por riesgo de sangrado por las varicosidades pelvianas y la segunda por indicación neurológica. Se obtuvieron en ambos casos recién nacidos femeninos, de 2620 y 3200 gramos respectivamente y en buenas condiciones.  Conclusiones: Debe realizarse una correcta anamnesis durante los controles prenatales para identificar los factores de riesgo que se relacionan con esta entidad que es poco frecuente, pero está relacionada con una gran morbilidad. Es indispensable la actuación en equipo y la evaluación integral de estos casos por un grupo especializado de angiólogos, ginecobstetras, anestesistas, cirujanos, clínicos, y de otras especialidades, para lograr un resultado óptimo.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT  Introduction:  Klippel Trenaunay Weber syndrome is a congenital vascular disease, of unknown causes, characterized by flat hemangiomas, overgrowth of bones and soft tissue, and varicose veins. When associated with pregnancy, it increases maternal and fetal morbidity and mortality.  Objective:  To describe two clinical cases of pregnant women with this syndrome, which were treated at the Ramón González Coro Gynecobstetric Teaching Hospital in Havana, Cuba.  Methods:  A descriptive, retrospective study of two cases using the information collection technique, analysis of the medical history, and search for updated literature. It was carried out in accordance with existing regulations and ethical principles for human research. Patients were not required to offer their informed consent.  Case reports:  The two cases presented were pregnant adolescents who were followed up in a multidisciplinary consultation and underwent caesarean section at 38 weeks, the first due to risk of bleeding as result of pelvic varicosities and the second due to neurological indication. In both cases, female newborns, 2620 and 3200 grams respectively, were obtained in good conditions.  Conclusions:  Correct anamnesis must be carried out during prenatal controls to identify the risk factors that are related to this entity, which is rare, but is related to high morbidity. Team action and comprehensive evaluation of these cases, by a specialized group of angiologists, gynecologists, anesthetists, surgeons, clinicians, and other specialties, are essential to achieve an optimal result.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Síndrome de Klippel Trenaunay Weber]]></kwd>
<kwd lng="es"><![CDATA[embarazo]]></kwd>
<kwd lng="es"><![CDATA[angiosteohipertrofia]]></kwd>
<kwd lng="es"><![CDATA[anomalía vascular]]></kwd>
<kwd lng="en"><![CDATA[Klippel Trenaunay Weber syndrome]]></kwd>
<kwd lng="en"><![CDATA[pregnancy]]></kwd>
<kwd lng="en"><![CDATA[angiosteohypertrophy]]></kwd>
<kwd lng="en"><![CDATA[vascular abnormality]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<label>1</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Pérez Elizondo]]></surname>
<given-names><![CDATA[AD]]></given-names>
</name>
<name>
<surname><![CDATA[Ruíz Pérez]]></surname>
<given-names><![CDATA[ME]]></given-names>
</name>
<name>
<surname><![CDATA[Contreras Guzmán]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Síndrome de Klippel Trenaunay, a propósito de un caso incipiente]]></article-title>
<source><![CDATA[Pediatría de México]]></source>
<year>2013</year>
<volume>15</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>54-6</page-range></nlm-citation>
</ref>
<ref id="B2">
<label>2</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Torres Farías]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
<name>
<surname><![CDATA[Torres Gómez]]></surname>
<given-names><![CDATA[LG]]></given-names>
</name>
<name>
<surname><![CDATA[Burciaga Sepúlveda]]></surname>
<given-names><![CDATA[AS]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Síndrome de Klippel-Trenaunay y embarazo. Comunicación de un caso]]></article-title>
<source><![CDATA[Ginecol Obstet Mex]]></source>
<year>2010</year>
<volume>78</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>287-90</page-range></nlm-citation>
</ref>
<ref id="B3">
<label>3</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Gundogan]]></surname>
<given-names><![CDATA[T]]></given-names>
</name>
<name>
<surname><![CDATA[Jacquemyn]]></surname>
<given-names><![CDATA[Y]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA["Klippel-Trenaunay Syndrome and Pregnancy,"]]></article-title>
<source><![CDATA[Obstetrics and Gynecology International]]></source>
<year>2010</year>
<volume>2010</volume>
<page-range>1-3</page-range></nlm-citation>
</ref>
<ref id="B4">
<label>4</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Castillo]]></surname>
<given-names><![CDATA[SD]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Somatic activating mutations in Pik3ca cause sporadic venous malformations in mice and humans]]></article-title>
<source><![CDATA[Sci Transl Med]]></source>
<year>2016</year>
<volume>30</volume>
<numero>8</numero>
<issue>8</issue>
<page-range>332-9</page-range></nlm-citation>
</ref>
<ref id="B5">
<label>5</label><nlm-citation citation-type="book">
<source><![CDATA[Klippel Trenaunay Syndrome]]></source>
<year>2016</year>
<publisher-loc><![CDATA[Rockville Pike ]]></publisher-loc>
<publisher-name><![CDATA[Genetics Home Reference]]></publisher-name>
</nlm-citation>
</ref>
<ref id="B6">
<label>6</label><nlm-citation citation-type="book">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Camila]]></surname>
<given-names><![CDATA[K]]></given-names>
</name>
<name>
<surname><![CDATA[Janniger]]></surname>
<given-names><![CDATA[MD]]></given-names>
</name>
<name>
<surname><![CDATA[Michael]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Wells]]></surname>
<given-names><![CDATA[MD]]></given-names>
</name>
</person-group>
<source><![CDATA[Klippel-Trenaunay-Weber Syndrome]]></source>
<year>2017</year>
<publisher-loc><![CDATA[New York ]]></publisher-loc>
<publisher-name><![CDATA[Medscape]]></publisher-name>
</nlm-citation>
</ref>
<ref id="B7">
<label>7</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Horbach]]></surname>
<given-names><![CDATA[SE]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Complications of pregnancy and labour in women with Klippel-Trenaunay syndrome: Nations wide cross sectional study]]></article-title>
<source><![CDATA[BJOG: An International Journal of Obstetrics &amp; Gynaecology]]></source>
<year>2017</year>
<volume>124</volume>
<numero>11</numero>
<issue>11</issue>
<page-range>1780-8</page-range></nlm-citation>
</ref>
<ref id="B8">
<label>8</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Rodríguez]]></surname>
<given-names><![CDATA[PL]]></given-names>
</name>
<name>
<surname><![CDATA[Hernández]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Crespo]]></surname>
<given-names><![CDATA[T]]></given-names>
</name>
<name>
<surname><![CDATA[Espín]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Síndrome de Klippel Trenaunay Weber. Consideraciones sobre un caso clínico]]></article-title>
<source><![CDATA[Rev. Med. Electrón]]></source>
<year>2018</year>
<volume>40</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>200-5</page-range></nlm-citation>
</ref>
<ref id="B9">
<label>9</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Nápoles Méndez]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Ying Rodríguez]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Nápoles Pastoriza]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Síndrome de Klippel-Trenaunay-Weber en una gestante]]></article-title>
<source><![CDATA[MEDISAN]]></source>
<year>2016</year>
<volume>20</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>77-83</page-range></nlm-citation>
</ref>
<ref id="B10">
<label>10</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Pérez de Alejo]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Hernández Negrín]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
<name>
<surname><![CDATA[Vázquez Gómez]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Síndrome de Klippel Trenaunay Weber complicado con trombosis venosa cerebral. Reporte de un caso]]></article-title>
<source><![CDATA[Cor Salud Rev Enf Cardiovasculares]]></source>
<year>2016</year>
<volume>8</volume>
<numero>4</numero>
<issue>4</issue>
</nlm-citation>
</ref>
<ref id="B11">
<label>11</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Chadha]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Management of Pregnancy with Klippel-Trenaunay-Weber Syndrome: A Case Report and Review]]></article-title>
<source><![CDATA[Case Reports in Obstetrics and Gynecology. Hindawi]]></source>
<year>2018</year>
<volume>18</volume>
<page-range>1-6</page-range></nlm-citation>
</ref>
<ref id="B12">
<label>12</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Gupta]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Sharma]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
<name>
<surname><![CDATA[Tomar]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Bhardwaj]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Pregnancy in a case of Klippel Trenaunay Syndrome: A Case Report and Review of Literature]]></article-title>
<source><![CDATA[JCR]]></source>
<year>2014</year>
<volume>4</volume>
<page-range>491-4</page-range></nlm-citation>
</ref>
<ref id="B13">
<label>13</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Arain]]></surname>
<given-names><![CDATA[Z]]></given-names>
</name>
<name>
<surname><![CDATA[Tiwari]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Nakhosteen]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[A rare case of Klippel Trenaunay Syndrome in pregnancy]]></article-title>
<source><![CDATA[Food Sci Nutr Res]]></source>
<year>2018</year>
<volume>1</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>1-3</page-range></nlm-citation>
</ref>
<ref id="B14">
<label>14</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Arun]]></surname>
<given-names><![CDATA[Keepanasseril]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Pregnancy in women with Klippel Trenaunay syndrome: Report of three pregnancies in a single patient and review of literature]]></article-title>
<source><![CDATA[Obstetric Medicine]]></source>
<year>2017</year>
<volume>10</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>177-82</page-range></nlm-citation>
</ref>
<ref id="B15">
<label>15</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Velázquez]]></surname>
<given-names><![CDATA[W]]></given-names>
</name>
<name>
<surname><![CDATA[Matos]]></surname>
<given-names><![CDATA[Y]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Enfoque Interdisciplinario en la Gestante con Síndrome de Klippel-Trenaunay-Weber]]></article-title>
<source><![CDATA[Revista Científica Hallazgos]]></source>
<year>2016</year>
<volume>21</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>79-84</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
