<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0864-2125</journal-id>
<journal-title><![CDATA[Revista Cubana de Medicina General Integral]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Cubana Med Gen Integr]]></abbrev-journal-title>
<issn>0864-2125</issn>
<publisher>
<publisher-name><![CDATA[ECIMED]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0864-21252022000400015</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Síndrome de Ehlers Danlos tipo III en un adolescente masculino]]></article-title>
<article-title xml:lang="en"><![CDATA[Ehlers-Danlos Syndrome Type III in a Male Adolescent]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Núñez López]]></surname>
<given-names><![CDATA[Marta Belkis]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Triana Alonso]]></surname>
<given-names><![CDATA[Pedro Gregorio]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Mederos Benítez]]></surname>
<given-names><![CDATA[Yendry]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad de Ciencias Médicas de Villa Clara  ]]></institution>
<addr-line><![CDATA[ Villa Clara]]></addr-line>
<country>Cuba</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2022</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2022</year>
</pub-date>
<volume>38</volume>
<numero>4</numero>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_arttext&amp;pid=S0864-21252022000400015&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_abstract&amp;pid=S0864-21252022000400015&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_pdf&amp;pid=S0864-21252022000400015&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN  Introducción:  El síndrome de Ehlers Danlos tipo III o síndrome de hiperlaxitud articular benigna, consiste en una alteración genética del colágeno tipo III/I con un patrón de herencia autosómico dominante, caracterizado por la presencia de articulaciones con una amplitud de movilidad incrementada y síntomas musculoesqueléticos y extraesqueléticos.  Objetivo:  Valorar la importancia de la aplicación del método clínico para el diagnóstico del Síndrome de Ehlers Danlos tipo III.  Caso clínico:  Se presenta el caso de un adolescente masculino de 15 años de edad con diagnóstico clínico reciente del Síndrome de Ehlers Danlos tipo III.  Conclusiones:  Para lograr un diagnóstico certero del síndrome de Ehlers Danlos tipo III es imprescindible aplicar con ciencia y conciencia el método clínico.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT  Introduction:  Ehlers-Danlos syndrome type III or benign joint hyperlaxity syndrome consists in a genetic alteration of collagen type III/I with a dominant autosomal inheritance pattern, characterized by the presence of joints with increased range of motion, as well as musculoskeletal and extraskeletal symptoms.  Objective:  To assess the importance of applying the clinical method for the diagnosis of Ehlers-Danlos syndrome type III.  Clinical case:  The case is presented of a 15-year-old male adolescent with a recent clinical diagnosis of Ehlers-Danlos syndrome type III.  Conclusions:  In order to achieve an accurate diagnosis of Ehlers-Danlos syndrome type III, it is essential to apply the clinical method scientifically and conscientiously.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[hipermovilidad articular]]></kwd>
<kwd lng="es"><![CDATA[hiperlaxitud articular]]></kwd>
<kwd lng="es"><![CDATA[Ehlers Danlos tipo III]]></kwd>
<kwd lng="en"><![CDATA[joint hypermobility]]></kwd>
<kwd lng="en"><![CDATA[joint hyperlaxity]]></kwd>
<kwd lng="en"><![CDATA[Ehlers-Danlos type III]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<label>1</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Reyes-Cadena]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[El niño con dolor de piernas]]></article-title>
<source><![CDATA[Acta Pediátrica de México]]></source>
<year>2016</year>
<volume>37</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>183-7</page-range></nlm-citation>
</ref>
<ref id="B2">
<label>2</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Gedalia]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Joint pain in children: an algorithmic approach]]></article-title>
<source><![CDATA[IMAJ]]></source>
<year>2002</year>
<volume>4</volume>
<numero>10</numero>
<issue>10</issue>
<page-range>837-42</page-range></nlm-citation>
</ref>
<ref id="B3">
<label>3</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Haro]]></surname>
<given-names><![CDATA[DM]]></given-names>
</name>
<name>
<surname><![CDATA[Morante]]></surname>
<given-names><![CDATA[RM]]></given-names>
</name>
<name>
<surname><![CDATA[Lillo]]></surname>
<given-names><![CDATA[SS]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Síndrome de hiperlaxitud articular benigno en el niño]]></article-title>
<source><![CDATA[Rev Med Clin Condes]]></source>
<year>2014</year>
<volume>25</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>255-64</page-range></nlm-citation>
</ref>
<ref id="B4">
<label>4</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Arbelo Figueredo]]></surname>
<given-names><![CDATA[MC]]></given-names>
</name>
<name>
<surname><![CDATA[Estévez Perera]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[González Méndez]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
<name>
<surname><![CDATA[Porro Novo]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Caracterización clínica y criterios diagnósticos en mujeres con hipermovilidad articular]]></article-title>
<source><![CDATA[Revista Cubana de Reumatología]]></source>
<year>2017</year>
<volume>19</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>57-64</page-range></nlm-citation>
</ref>
<ref id="B5">
<label>5</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Suárez Ayala]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[María Valencia]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Gómez Mora]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Relación entre hipermovilidad articular generalizada y dolor articular en niños de 4 a 17 años en Pasto, Colombia]]></article-title>
<source><![CDATA[Rev Colomb Reumatol]]></source>
<year>2015</year>
<volume>22</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>10-21</page-range></nlm-citation>
</ref>
<ref id="B6">
<label>6</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Larrain]]></surname>
<given-names><![CDATA[MV]]></given-names>
</name>
<name>
<surname><![CDATA[Di Rocco]]></surname>
<given-names><![CDATA[EL]]></given-names>
</name>
<name>
<surname><![CDATA[Riatti]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
<name>
<surname><![CDATA[Vallone]]></surname>
<given-names><![CDATA[MG]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Hiperlaxitud articular e inestabilidad de hombro. Tratamiento artroscópico de la inestabilidad multidireccional]]></article-title>
<source><![CDATA[Rev Artroscopia]]></source>
<year>2012</year>
<volume>19</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>12-7</page-range></nlm-citation>
</ref>
<ref id="B7">
<label>7</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Menéndez Alejo]]></surname>
<given-names><![CDATA[FM]]></given-names>
</name>
<name>
<surname><![CDATA[Díaz Lazaga]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Torrez Cárdenas]]></surname>
<given-names><![CDATA[V]]></given-names>
</name>
<name>
<surname><![CDATA[Martínez Rodríguez]]></surname>
<given-names><![CDATA[V]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Síndrome de hipermovilidad articular en una población juvenil cubana]]></article-title>
<source><![CDATA[Rev Reumatol Clin]]></source>
<year>2009</year>
<volume>5</volume>
<numero>6</numero>
<issue>6</issue>
<page-range>244-7</page-range></nlm-citation>
</ref>
<ref id="B8">
<label>8</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Puerto Martínez]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Caracterización clínica y manejo del síndrome de Ehlers Danlos]]></article-title>
<source><![CDATA[Rev Ciencias Médicas]]></source>
<year>2017</year>
<volume>21</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>124-50</page-range></nlm-citation>
</ref>
<ref id="B9">
<label>9</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Farro-Uceda]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Tapia-Egoavil]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Valverde-Tarazona]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
<name>
<surname><![CDATA[Bautista-Chirinos]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Amaya-Solís]]></surname>
<given-names><![CDATA[K]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Relación entre hiperlaxitud articular, dismetría de miembros inferiores y control postural con los trastornos posturales]]></article-title>
<source><![CDATA[Rev Med Hered]]></source>
<year>2016</year>
<volume>27</volume>
<page-range>216-22</page-range></nlm-citation>
</ref>
<ref id="B10">
<label>10</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Pailhez]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Meroño]]></surname>
<given-names><![CDATA[O]]></given-names>
</name>
<name>
<surname><![CDATA[Agulló]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Bulbena]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Relación entre presión arterial y laxitud articular]]></article-title>
<source><![CDATA[Rev Med Clin (Barc)]]></source>
<year>2011</year>
<volume>136</volume>
<numero>11</numero>
<issue>11</issue>
<page-range>504-7</page-range></nlm-citation>
</ref>
<ref id="B11">
<label>11</label><nlm-citation citation-type="book">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Hernández Huamán]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
</person-group>
<source><![CDATA[Tratamiento fisioterapéutico en el síndrome de hipermovilidad articular. Colecciones Terapia Física y Rehabilitación]]></source>
<year>2017</year>
<publisher-name><![CDATA[Repositorio de la Universidad INCA Garcilaso de la Vega]]></publisher-name>
</nlm-citation>
</ref>
</ref-list>
</back>
</article>
