<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0864-2176</journal-id>
<journal-title><![CDATA[Revista Cubana de Oftalmología]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Cubana Oftalmol]]></abbrev-journal-title>
<issn>0864-2176</issn>
<publisher>
<publisher-name><![CDATA[Editorial Ciencias Médicas]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0864-21762022000100013</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Retinopatía del prematuro con presentación atípica]]></article-title>
<article-title xml:lang="en"><![CDATA[Retinopathy of prematurity with atypical presentation]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Casanueva Cabeza]]></surname>
<given-names><![CDATA[Haymy Caridad]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Toledo González]]></surname>
<given-names><![CDATA[Yusimik]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Blanco Mesa]]></surname>
<given-names><![CDATA[Eglys]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Pérez de la Rosa]]></surname>
<given-names><![CDATA[Maibi]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Alemañy Rubio]]></surname>
<given-names><![CDATA[Ernesto]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Instituto Cubano de Oftalmología Ramón Pando Ferrer  ]]></institution>
<addr-line><![CDATA[ La Habana]]></addr-line>
<country>Cuba</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>03</month>
<year>2022</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>03</month>
<year>2022</year>
</pub-date>
<volume>35</volume>
<numero>1</numero>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_arttext&amp;pid=S0864-21762022000100013&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_abstract&amp;pid=S0864-21762022000100013&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_pdf&amp;pid=S0864-21762022000100013&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN La retinopatía de la prematuridad es una enfermedad dinámica vasoproliferativa de la retina inmadura postnatal que afecta a los bebés prematuros. Cuando aparecen signos de atipicidad en su diagnóstico o evolución deben descartarse otras entidades vasculares de la retina, que generalmente tienen un trasfondo genético y semejan o coexisten con dicha entidad. Se presenta un caso con características de Retinopatía del prematuro y algunos signos de atipicidad. Se describe su manejo y evolución, así como una breve descripción de las entidades que conforman el diagnóstico diferencial.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT Retinopathy of prematurity is a dynamic vasoproliferative disease of the immature postnatal retina that affects premature babies. When signs of atypicality appear in its diagnosis or evolution, other vascular entities of the retina must be ruled out, which generally have a genetic background and resemble or coexist with said entity. We present a case with characteristics of Retinopathy of prematurity and some signs of atypicality. Its management and evolution are described, as well as a brief description of the entities that make up the differential diagnosis.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[retinopatía de la prematuridad]]></kwd>
<kwd lng="es"><![CDATA[incontinencia pigmenti]]></kwd>
<kwd lng="es"><![CDATA[enfermedad de norrie]]></kwd>
<kwd lng="es"><![CDATA[enfermedad de coats]]></kwd>
<kwd lng="es"><![CDATA[vitreorretinopatía exudativa familiar]]></kwd>
<kwd lng="es"><![CDATA[ROPER]]></kwd>
<kwd lng="en"><![CDATA[retinopathy of prematurity]]></kwd>
<kwd lng="en"><![CDATA[pigmenti incontinence]]></kwd>
<kwd lng="en"><![CDATA[norrie's disease]]></kwd>
<kwd lng="en"><![CDATA[coats disease]]></kwd>
<kwd lng="en"><![CDATA[familial exudative vitreoretinopathy]]></kwd>
<kwd lng="en"><![CDATA[ROPER]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<label>1</label><nlm-citation citation-type="">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Silva]]></surname>
<given-names><![CDATA[JC]]></given-names>
</name>
<name>
<surname><![CDATA[Vázquez de]]></surname>
<given-names><![CDATA[Kartzow]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Visión panamericana de la retinopatía del prematuro]]></article-title>
<source><![CDATA[Retinopatía del Prematuro]]></source>
<year>2019</year>
<edition>Permanyer</edition>
<page-range>1-4</page-range></nlm-citation>
</ref>
<ref id="B2">
<label>2</label><nlm-citation citation-type="book">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Amphornphruet]]></surname>
<given-names><![CDATA[Atchara]]></given-names>
</name>
<name>
<surname><![CDATA[Audina]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Berrocal. Familial Exudative Vitreoretinopathy or Retinopathy of Prematurity]]></article-title>
<source><![CDATA[A Quick Guide to Pediatric Retina]]></source>
<year>2021</year>
<page-range>53-8</page-range><publisher-name><![CDATA[Springer]]></publisher-name>
</nlm-citation>
</ref>
<ref id="B3">
<label>3</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Drenser]]></surname>
<given-names><![CDATA[KA]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Wnt signaling pathway in retinal vascularization]]></article-title>
<source><![CDATA[Eye Brain]]></source>
<year>2016</year>
<volume>8</volume>
<page-range>141-6</page-range></nlm-citation>
</ref>
<ref id="B4">
<label>4</label><nlm-citation citation-type="">
<source><![CDATA[Wnt Signaling in vascular eye diseases Progress in Retinal and Eye Research]]></source>
<year>2019</year>
<volume>70</volume>
<page-range>110-33</page-range></nlm-citation>
</ref>
<ref id="B5">
<label>5</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Kondo]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
<name>
<surname><![CDATA[Kusaka]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Yoshinaga]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Genetic variants of FZD4 and LRP5 genes in patients with advanced retinopathy of prematurity]]></article-title>
<source><![CDATA[Mol Vis]]></source>
<year>2013</year>
<volume>19</volume>
<page-range>476-85</page-range></nlm-citation>
</ref>
<ref id="B6">
<label>6</label><nlm-citation citation-type="book">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Li]]></surname>
<given-names><![CDATA[Yian]]></given-names>
</name>
<name>
<surname><![CDATA[Li]]></surname>
<given-names><![CDATA[Jiakai]]></given-names>
</name>
<name>
<surname><![CDATA[Zhang]]></surname>
<given-names><![CDATA[Xiang]]></given-names>
</name>
<name>
<surname><![CDATA[Peng]]></surname>
<given-names><![CDATA[Jie]]></given-names>
</name>
<name>
<surname><![CDATA[Li]]></surname>
<given-names><![CDATA[Jing]]></given-names>
</name>
<name>
<surname><![CDATA[Zhao]]></surname>
<given-names><![CDATA[Peiquan]]></given-names>
</name>
</person-group>
<source><![CDATA[Identification of Gene Mutations in Atypical Retinopathy of Prematurity Cases]]></source>
<year>2020</year>
<publisher-name><![CDATA[Journal of Ophthalmology]]></publisher-name>
</nlm-citation>
</ref>
<ref id="B7">
<label>7</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Portuondo Barbarrosa]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Incontinencia pigmenti y manifestaciones neurológicas]]></article-title>
<source><![CDATA[Revista Cubana de Pediatría]]></source>
<year>2018</year>
<volume>90</volume>
<numero>2</numero>
<issue>2</issue>
</nlm-citation>
</ref>
<ref id="B8">
<label>8</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[García Rodríguez]]></surname>
<given-names><![CDATA[Y]]></given-names>
</name>
<name>
<surname><![CDATA[Castillo Maspons]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Incontinencia pigmenti en un recién nacido Presentación de un caso]]></article-title>
<source><![CDATA[Medisur]]></source>
<year>2015</year>
<volume>13</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>555-9</page-range></nlm-citation>
</ref>
<ref id="B9">
<label>9</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Cortés]]></surname>
<given-names><![CDATA[Carolina Ivette]]></given-names>
</name>
<name>
<surname><![CDATA[Cardozo]]></surname>
<given-names><![CDATA[Ana Bolena]]></given-names>
</name>
<name>
<surname><![CDATA[Barrera]]></surname>
<given-names><![CDATA[Juan Camilo]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Incontinencia pigmentaria: un caso típico]]></article-title>
<source><![CDATA[Dermatol Rev Mex]]></source>
<year>2015</year>
<volume>59</volume>
<page-range>546-51</page-range></nlm-citation>
</ref>
<ref id="B10">
<label>10</label><nlm-citation citation-type="">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Cammarata-Scalisia]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
<name>
<surname><![CDATA[Fuscob]]></surname>
<given-names><![CDATA[MV.]]></given-names>
</name>
</person-group>
<source><![CDATA[Ursinib Incontinencia pigmenti]]></source>
<year>2019</year>
<volume>110</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>273-8</page-range></nlm-citation>
</ref>
<ref id="B11">
<label>11</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Santana Hernández]]></surname>
<given-names><![CDATA[EE]]></given-names>
</name>
<name>
<surname><![CDATA[Tamayo Chang]]></surname>
<given-names><![CDATA[VJ]]></given-names>
</name>
<name>
<surname><![CDATA[Marrero Infante]]></surname>
<given-names><![CDATA[JM]]></given-names>
</name>
<name>
<surname><![CDATA[Márquez Ibáñez]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
<name>
<surname><![CDATA[Artigas Cuenca]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Presentación de un paciente con enfermedad de Norrie]]></article-title>
<source><![CDATA[CCM]]></source>
<year>2013</year>
<volume>17</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>397-402</page-range></nlm-citation>
</ref>
<ref id="B12">
<label>12</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Messina Baas O]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Cuevas Covarrubias]]></surname>
<given-names><![CDATA[SA]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Enfermedad de Norrie]]></article-title>
<source><![CDATA[Presentación de un caso familiar]]></source>
<year>2005</year>
<volume>79</volume>
<numero>1</numero>
<issue>1</issue>
</nlm-citation>
</ref>
<ref id="B13">
<label>13</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Jalilo Hernández]]></surname>
<given-names><![CDATA[SM]]></given-names>
</name>
<name>
<surname><![CDATA[Santander Acosta]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Gómez Martínez]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Enfermedad de Coats]]></article-title>
<source><![CDATA[Rev Ciencias Médicas]]></source>
<year>2020</year>
<volume>24</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>281-6</page-range></nlm-citation>
</ref>
<ref id="B14">
<label>14</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Antonio Ramos-Suárez]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Gismero-Moreno]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Tirado-Carmona]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Lorenzo-Soto]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[García-Martín]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Diagnóstico casual de vitreorretinopatía exudativa familiar en 2 hermanos asintomáticos Estudio de imagen de campo amplio y anormalidades retinianas objetivadas en el polo posterior]]></article-title>
<source><![CDATA[Rev Mex Oftalmol]]></source>
<year>2018</year>
<volume>92</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>43-9</page-range></nlm-citation>
</ref>
<ref id="B15">
<label>15</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[John]]></surname>
<given-names><![CDATA[VJ]]></given-names>
</name>
<name>
<surname><![CDATA[McClintic]]></surname>
<given-names><![CDATA[JI]]></given-names>
</name>
<name>
<surname><![CDATA[Hess]]></surname>
<given-names><![CDATA[DJ]]></given-names>
</name>
<name>
<surname><![CDATA[Berrocal]]></surname>
<given-names><![CDATA[AM]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Retinopathy of Prematurity Versus Familial Exudative Vitreoretinopathy Report on Clinical and Angiographic Findings]]></article-title>
<source><![CDATA[Ophthalmic Surg Lasers Imaging Retina]]></source>
<year>2016</year>
<volume>47</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>14-9</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
