<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1025-0255</journal-id>
<journal-title><![CDATA[Revista Archivo Médico de Camagüey]]></journal-title>
<abbrev-journal-title><![CDATA[AMC]]></abbrev-journal-title>
<issn>1025-0255</issn>
<publisher>
<publisher-name><![CDATA[Universidad de Ciencias Médicas de Camagüey]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1025-02552019000100104</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Cirrosis hepática y fibrosis quística en un paciente pediátrico]]></article-title>
<article-title xml:lang="en"><![CDATA[Hepatic cirrhosis and cystic fibrosis in pediatric patients]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Reyes-Escobar]]></surname>
<given-names><![CDATA[Ana Dianelis]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Carmenates-Álvarez]]></surname>
<given-names><![CDATA[Bárbara Maitee]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Peña-Borroto]]></surname>
<given-names><![CDATA[Yamilka Joamis]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Trujillo-Pérez]]></surname>
<given-names><![CDATA[Yon Luis]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rojas-Peláez]]></surname>
<given-names><![CDATA[Yosvany]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad de Ciencias Médicas de Camagüey Hospital Pediátrico Universitario Eduardo Agramonte Piña ]]></institution>
<addr-line><![CDATA[Camagüey ]]></addr-line>
<country>Cuba</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidad de Ciencias Médicas de Camagüey Hospital Universitario Amalia Simoni ]]></institution>
<addr-line><![CDATA[Camagüey ]]></addr-line>
<country>Cuba</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Universidad de Ciencias Médicas de Camagüey Policlínico Docente José Martí ]]></institution>
<addr-line><![CDATA[Camagüey ]]></addr-line>
<country>Cuba</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>02</month>
<year>2019</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>02</month>
<year>2019</year>
</pub-date>
<volume>23</volume>
<numero>1</numero>
<fpage>104</fpage>
<lpage>111</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_arttext&amp;pid=S1025-02552019000100104&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_abstract&amp;pid=S1025-02552019000100104&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_pdf&amp;pid=S1025-02552019000100104&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN  Fundamento: aunque la enfermedad hepática crónica como complicación de la fibrosis quística ha sido eclipsada por otros signos y síntomas más obvios a nivel respiratorio y pancreático, constituye la segunda causa de muerte en los pacientes con fibrosis quística.  Objetivo: presentar el caso de una transicional de tres años con hepatomegalia y pruebas analíticas hepáticas alteradas como manifestaciones iniciales de la fibrosis quística.  Caso clínico: paciente de tres años, femenina, con historia de distensión abdominal, hepatomegalia y desnutrición. Por esta sintomatología es remitida a la consulta de Gastroenterología.  Conclusiones: se debe sospechar la fibrosis quística en pacientes pediátricos con hepatopatía crónica. Se observó mejoría clínica de las manifestaciones respiratorias y del estado nutricional, sin embargo, la hepatopatía evolucionó a la cirrosis hepática establecida.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT  Background:  although the chronic hepatic illness as complication of the cystic fibrosis has been eclipsed by other signs and more obvious symptoms at breathing and pancreatic level, is the second cause of death in the patients with cystic fibrosis.  Objective:  to present the case of a three year-old transitional one with hepatomegaly and hepatic analytic tests altered as initial manifestations of the cystic fibrosis.  Clinical case: a three-year old, female patient with history of abdominal distension, hepatomegaly, and malnutrition. For this symptoms, she is remitted to the Gastroenterology consultation.  Conclusions:  the cystic fibrosis should be suspected in pediatric patient with chronic hepatic diseases. Clinical improvement of the breathing manifestations was observed and of the nutritional state, however the chronic hepatic disease evolved to the established hepatic cirrhosis.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[HEPATOMEGALIA]]></kwd>
<kwd lng="es"><![CDATA[FIBROSIS QUÍSTICA/mortalidad]]></kwd>
<kwd lng="es"><![CDATA[FIBROSIS QUÍSTICA/complicaciones]]></kwd>
<kwd lng="es"><![CDATA[CIRROSIS HEPÁTICA/complicaciones]]></kwd>
<kwd lng="es"><![CDATA[PREESCOLAR]]></kwd>
<kwd lng="en"><![CDATA[HEPATOMEGALY]]></kwd>
<kwd lng="en"><![CDATA[CYSTIC FIBROSIS/mortality]]></kwd>
<kwd lng="en"><![CDATA[CYSTIC FIBROSIS/complications]]></kwd>
<kwd lng="en"><![CDATA[LIVER CIRRHOSIS/complications]]></kwd>
<kwd lng="en"><![CDATA[CHILD, PRESCHOOL]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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