<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1028-9933</journal-id>
<journal-title><![CDATA[Revista Información Científica]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. inf. cient.]]></abbrev-journal-title>
<issn>1028-9933</issn>
<publisher>
<publisher-name><![CDATA[Universidad de Ciencias Médicas Guantánamo]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1028-99332025000100002</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Abordaje de la vía aérea en paciente pediátrico con síndrome de Noonan. Presentación de un caso]]></article-title>
<article-title xml:lang="en"><![CDATA[Airway approach in a pediatric patient with Noonan syndrome. Presentation of a case]]></article-title>
<article-title xml:lang="pt"><![CDATA[Abordagem das vias aéreas em paciente pediátrico com síndrome de Noonan. Apresentação de um caso]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[García-Jiménez]]></surname>
<given-names><![CDATA[Dayane]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Álvarez-Pérez]]></surname>
<given-names><![CDATA[Rolando Javier]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Fajardo-Alcalá]]></surname>
<given-names><![CDATA[Robin]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Corría-Milán]]></surname>
<given-names><![CDATA[Ivanis Idael]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad de Ciencias Médicas de Granma Hospital Pediátrico Provincial Hermanos Cordovés ]]></institution>
<addr-line><![CDATA[ Granma]]></addr-line>
<country>Cuba</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidad de Ciencias Médicas de Granma  ]]></institution>
<addr-line><![CDATA[ Granma]]></addr-line>
<country>Cuba</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>00</month>
<year>2025</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>00</month>
<year>2025</year>
</pub-date>
<volume>104</volume>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_arttext&amp;pid=S1028-99332025000100002&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_abstract&amp;pid=S1028-99332025000100002&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_pdf&amp;pid=S1028-99332025000100002&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN El síndrome de Noonan es una enfermedad congénita, de particular interés para el anestesiólogo por ser considerado probable vía aérea difícil.Se presentó un paciente masculino de 13 años con antecedentes patológicos personales de síndrome de Noonan genotipo PTPN11, hipotiroidismo, discapacidad intelectual ligeraque acudió a Cuerpo de Guardia de Cirugía por presentar dolor abdominal de 16 horas de evolución. Fue diagnosticado con apendicitis aguda y se anunció para apendicectomía de urgencia.La presencia del síndrome de Noonan en el paciente requirió un enfoque anestésico personalizado para manejar las posibles complicaciones transoperatorias. La planificación preoperatoria meticulosa, la elección de la secuencia rápida para la inducción anestésica y la monitorización rigurosa fueron clave para el éxito de la cirugía.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT Noonan syndrome is a congenital of particular interest to the anesthesiologist because it is considered a probable difficult airway. A 13-year-old male patient was presented with a personal pathological history of Noonan syndrome genotype PTPN11, hypothyroidism, mild intellectual disability who attended the Surgical Guard Corps due to abdominal pain of 16 hours duration. He was diagnosed with acute appendicitis and was scheduled for emergency appendectomy. The presence of Noonan syndrome in the patient required a personalized anesthetic approach to manage potential intraoperative complications. Meticulous preoperative planning, the choice of rapid sequence for anesthetic induction, and rigorous monitoring were key to the success of the surgery.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[RESUMO A síndrome de Noonan é uma doença congênita causada por uma mutação autossômica dominante. Essa síndrome é de particular interesse para o anestesiologista por ser considerada uma provável via aérea difícil. Paciente do sexo masculino, 13 anos, apresentou história patológica pessoal de síndrome de Noonan, genótipo PTPN11, hipotireoidismo e deficiência intelectual leve, que compareceu ao Corpo de Guardas Cirúrgicos devido a dor abdominal com duração de 16 horas. Ele foi diagnosticado com apendicite aguda e foi agendado para apendicectomia de emergência. A presença da síndrome de Noonan no paciente exigiu abordagem anestésica personalizada para manejo de possíveis complicações intraoperatórias. O planejamento pré-operatório meticuloso, a escolha da sequência rápida para indução anestésica e o acompanhamento rigoroso foram fundamentais para o sucesso da cirurgia.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[anestesia]]></kwd>
<kwd lng="es"><![CDATA[defecto congénito]]></kwd>
<kwd lng="es"><![CDATA[enfermedad genética]]></kwd>
<kwd lng="es"><![CDATA[intubación]]></kwd>
<kwd lng="es"><![CDATA[rasopatía]]></kwd>
<kwd lng="es"><![CDATA[síndrome de Noonan]]></kwd>
<kwd lng="es"><![CDATA[vía aérea]]></kwd>
<kwd lng="es"><![CDATA[vía aérea difícil]]></kwd>
<kwd lng="en"><![CDATA[anesthesia]]></kwd>
<kwd lng="en"><![CDATA[congenital defect]]></kwd>
<kwd lng="en"><![CDATA[genetic disease]]></kwd>
<kwd lng="en"><![CDATA[intubation]]></kwd>
<kwd lng="en"><![CDATA[rasopathy]]></kwd>
<kwd lng="en"><![CDATA[Noonan syndrome]]></kwd>
<kwd lng="en"><![CDATA[airway]]></kwd>
<kwd lng="en"><![CDATA[difficult airway]]></kwd>
<kwd lng="pt"><![CDATA[anestesia]]></kwd>
<kwd lng="pt"><![CDATA[defeito congênito]]></kwd>
<kwd lng="pt"><![CDATA[doença genética]]></kwd>
<kwd lng="pt"><![CDATA[intubação]]></kwd>
<kwd lng="pt"><![CDATA[rasopatia]]></kwd>
<kwd lng="pt"><![CDATA[Síndrome de Noonan]]></kwd>
<kwd lng="pt"><![CDATA[via aérea]]></kwd>
<kwd lng="pt"><![CDATA[via aérea difícil]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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