<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1029-3019</journal-id>
<journal-title><![CDATA[MEDISAN]]></journal-title>
<abbrev-journal-title><![CDATA[MEDISAN]]></abbrev-journal-title>
<issn>1029-3019</issn>
<publisher>
<publisher-name><![CDATA[Centro Provincial de Información de Ciencias Médicas]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1029-30192018000700552</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Síndrome de Mayer-Rokitansky-Küster-Hauser o agenesia de útero y vagina en una paciente joven]]></article-title>
<article-title xml:lang="en"><![CDATA[Mayer-Rokitansky-Küster-Hauser Syndrome or uterus and vagina agenesis in a young patient]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Baral Ross]]></surname>
<given-names><![CDATA[Juana Himilce]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Orozco Hechavarría]]></surname>
<given-names><![CDATA[Nélida]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Prades Hung]]></surname>
<given-names><![CDATA[Eliecer]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad de Ciencias Médicas Hospital Materno Norte &#8220;Tamara Bunke Bider&#8221; ]]></institution>
<addr-line><![CDATA[Santiago de Cuba ]]></addr-line>
<country>Cuba</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidad de Ciencias Médicas Facultad de Ciencias Médicas No.1 ]]></institution>
<addr-line><![CDATA[Santiago de Cuba ]]></addr-line>
<country>Cuba</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>08</month>
<year>2018</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>08</month>
<year>2018</year>
</pub-date>
<volume>22</volume>
<numero>7</numero>
<fpage>552</fpage>
<lpage>558</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_arttext&amp;pid=S1029-30192018000700552&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_abstract&amp;pid=S1029-30192018000700552&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_pdf&amp;pid=S1029-30192018000700552&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN Se describe el caso clínico de una paciente con síndrome de Mayer-Rokitansky-Küster-Hauser o agenesia de útero y vagina, pero con ovarios funcionantes, atendida por un equipo multidisciplinario en el Hospital Materno Norte &#8220;Tamara Bunke Bider&#8221; de Santiago de Cuba, cuyo diagnóstico se realizó a través del examen físico, el antecedente de amenorrea primaria y estudios complementarios como el cariotipo y la resonancia magnética de la pelvis.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT The case report of a patient with syndrome of Mayer-Rokitansky-Küster-Hauser or uterus and vagina agenesis, but with functioning ovaries, assisted by a multidisciplinary team in "Tamara Bunke Bider" Northern Maternal Hospital in Santiago de Cuba, whose diagnosis was carried out through the physical exam, the history of primary amenorrhoea and complementary studies as the cariotype and magnetic resonance of the pelvis is described.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[síndrome de Mayer-Rokitansky-Küster-Hauser]]></kwd>
<kwd lng="es"><![CDATA[agenesia de útero y vagina]]></kwd>
<kwd lng="es"><![CDATA[agenesia mülleriana]]></kwd>
<kwd lng="es"><![CDATA[hospital materno]]></kwd>
<kwd lng="en"><![CDATA[Mayer-Rokitansky-Küster-Hauser syndrome]]></kwd>
<kwd lng="en"><![CDATA[uterus and vagina agenesis]]></kwd>
<kwd lng="en"><![CDATA[mülleriana agenesis]]></kwd>
<kwd lng="en"><![CDATA[maternal hospital]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<label>1</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Dias Nunes]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Lemos Zanatta]]></surname>
<given-names><![CDATA[DA]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Mayer- Rokitansky-Kuster Hauser Symdrome Casse report nuunes and Zanatta]]></article-title>
<source><![CDATA[Obstet Gynecol Cases Rev]]></source>
<year>2015</year>
<volume>2</volume>
<page-range>3</page-range></nlm-citation>
</ref>
<ref id="B2">
<label>2</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Álvarez Navarro]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Cabrera Carranco]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
<name>
<surname><![CDATA[Hernández Estrada]]></surname>
<given-names><![CDATA[AI]]></given-names>
</name>
<name>
<surname><![CDATA[Aguirre Oselle]]></surname>
<given-names><![CDATA[X]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Síndrome de Mayer-Rokitansky-Küster Reporte de un caso y revisión de la bibliografía relacionada con su tratamiento]]></article-title>
<source><![CDATA[Ginecol Obstet Mex]]></source>
<year>2012</year>
<volume>80</volume>
<numero>7</numero>
<issue>7</issue>
<page-range>473-9</page-range></nlm-citation>
</ref>
<ref id="B3">
<label>3</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Muńoz]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Trastornos menstruales en la adolescencia]]></article-title>
<source><![CDATA[Rev Chil Pediatr]]></source>
<year>1999</year>
<volume>70</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>250-6</page-range></nlm-citation>
</ref>
<ref id="B4">
<label>4</label><nlm-citation citation-type="">
<person-group person-group-type="author">
<name>
<surname><![CDATA[López Masó]]></surname>
<given-names><![CDATA[IM]]></given-names>
</name>
<name>
<surname><![CDATA[Trinchet Soler]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Ricardo Pérez]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Quintero Nicot]]></surname>
<given-names><![CDATA[W]]></given-names>
</name>
<name>
<surname><![CDATA[Cordovés Alamaquer]]></surname>
<given-names><![CDATA[Y]]></given-names>
</name>
</person-group>
<source><![CDATA[Asociación síndrome Vacterel con Mayer-Rokistanky-Kuster- Hauser. A propósito de un caso. Primer Congreso Virtual de Cirugía Pediátrica]]></source>
<year>2013</year>
</nlm-citation>
</ref>
<ref id="B5">
<label>5</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Barrecheguren Oliver]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
<name>
<surname><![CDATA[Álvarez Álvarez]]></surname>
<given-names><![CDATA[JI]]></given-names>
</name>
<name>
<surname><![CDATA[Bermejo Aycart]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Martínez Izquierdo]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Presentación atípica del síndrome de Rokitansky-Mayer-Küster-Hauser A propósito de un caso]]></article-title>
<source><![CDATA[Toko Ginecol Pract]]></source>
<year>1998</year>
<volume>57</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>194-8</page-range></nlm-citation>
</ref>
<ref id="B6">
<label>6</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Álvarez Uria]]></surname>
<given-names><![CDATA[MJ]]></given-names>
</name>
<name>
<surname><![CDATA[Sáiz]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Álvarez Montes]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
<name>
<surname><![CDATA[Santamarta]]></surname>
<given-names><![CDATA[ME]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Displasias vertebrales múltiples, asociadas al síndrome de Rokistanky una causa poco frecuente de escoliosis congénita. A propósito de un caso]]></article-title>
<source><![CDATA[Rehabilitación]]></source>
<year>2010</year>
<volume>44</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>261-6</page-range></nlm-citation>
</ref>
<ref id="B7">
<label>7</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[González Marino]]></surname>
<given-names><![CDATA[MA]]></given-names>
</name>
<name>
<surname><![CDATA[Pérez Solano]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Leiomioma uterino en una paciente con síndrome de Rokitansky-Mayer-Küster-Hauser Reporte de un caso]]></article-title>
<source><![CDATA[Rev Colombiana Obstet Ginecol]]></source>
<year>2010</year>
<volume>61</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>359-62</page-range></nlm-citation>
</ref>
<ref id="B8">
<label>8</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Vidyashree]]></surname>
<given-names><![CDATA[PG]]></given-names>
</name>
<name>
<surname><![CDATA[Muralidhar]]></surname>
<given-names><![CDATA[PV]]></given-names>
</name>
<name>
<surname><![CDATA[Jayaram]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
<name>
<surname><![CDATA[Latha]]></surname>
<given-names><![CDATA[K]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Rokitansky-Mayer-Küster-Hauser syndrome with multiple leimyomas]]></article-title>
<source><![CDATA[Int J Gynaecol Obstet]]></source>
<year>2015</year>
<volume>128</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>270-1</page-range></nlm-citation>
</ref>
<ref id="B9">
<label>9</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Arce Segura]]></surname>
<given-names><![CDATA[LJ]]></given-names>
</name>
<name>
<surname><![CDATA[Rodríguez de Mingo]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
<name>
<surname><![CDATA[Díaz Vera]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
<name>
<surname><![CDATA[García Sánchez]]></surname>
<given-names><![CDATA[V]]></given-names>
</name>
<name>
<surname><![CDATA[Calle Romero]]></surname>
<given-names><![CDATA[Y]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Síndrome de Mayer Rokitasnky-Kuster-Hauser A proposito de un caso]]></article-title>
<source><![CDATA[Semergen]]></source>
<year>2016</year>
<volume>42</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>50-2</page-range></nlm-citation>
</ref>
<ref id="B10">
<label>10</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Páez López]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[De los Ríos Posada]]></surname>
<given-names><![CDATA[JF]]></given-names>
</name>
<name>
<surname><![CDATA[Arango Martínez]]></surname>
<given-names><![CDATA[AD]]></given-names>
</name>
<name>
<surname><![CDATA[Castańeda Roldán]]></surname>
<given-names><![CDATA[JD]]></given-names>
</name>
<name>
<surname><![CDATA[Serna Agudelo]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
<name>
<surname><![CDATA[Vázquez Ruiz]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Manejo laparoscópico de miomatosis uterina en paciente con síndrome de Rokitansky Reporte de un caso y revisión de la literatura]]></article-title>
<source><![CDATA[Rev Colombiana Obstetr Ginecol]]></source>
<year>2013</year>
<volume>64</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>469-74</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
