<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1561-3194</journal-id>
<journal-title><![CDATA[Revista de Ciencias Médicas de Pinar del Río]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Ciencias Médicas]]></abbrev-journal-title>
<issn>1561-3194</issn>
<publisher>
<publisher-name><![CDATA[Editorial Ciencias Médicas]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1561-31942021000200017</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Síndrome de Sjögren juvenil con acidosis tubular renal distal de debut]]></article-title>
<article-title xml:lang="en"><![CDATA[Juvenile Sjögren&#8217;s syndrome with a presentation of renal distal tubular acidosis]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rodríguez Matanzas]]></surname>
<given-names><![CDATA[Didier]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Cruz García]]></surname>
<given-names><![CDATA[Yanet]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Urquiaga Rosa]]></surname>
<given-names><![CDATA[Juan Roney]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad de Ciencias Médicas de Pinar del Río Hospital Clínico Quirúrgico Docente León Cuervo Rubio ]]></institution>
<addr-line><![CDATA[Pinar del Río ]]></addr-line>
<country>Cuba</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidad de Ciencias Médicas de Pinar del Río. Hospital Pediátrico Provincial Pepe Portilla ]]></institution>
<addr-line><![CDATA[Pinar del Río ]]></addr-line>
<country>Cuba</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>04</month>
<year>2021</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>04</month>
<year>2021</year>
</pub-date>
<volume>25</volume>
<numero>2</numero>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_arttext&amp;pid=S1561-31942021000200017&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_abstract&amp;pid=S1561-31942021000200017&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_pdf&amp;pid=S1561-31942021000200017&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN  Introducción:  el Síndrome de Sjögren es una exocrinopatía autoinmune caracterizada por un infiltrado inflamatorio, con predominio de linfocitos en glándulas exocrinas y tejidos extraglandulares. La lesión glandular se caracteriza por la hiposecreción en mucosa oral y ocular.  Caso Clínico:  paciente femenina de 13 años de edad, procedente del municipio de Consolación del Sur, en la provincia de Pinar del Río, con Síndrome de Sjögren, cuya manifestación clínica inicial fue extraglandular, con el riñón como principal órgano afectado bajo la forma de acidosis tubular renal distal tipo I.  Conclusiones:  se demuestra que la realización de una minuciosa anamnesis, exploración clínica y la utilización de distintas herramientas diagnósticas, hacen posible un diagnóstico precoz de la enfermedad y de sus manifestaciones extraglandulares.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT  Introduction:  the Syndrome of Sjögren is an exocrinopatía autoinmune characterized by an infiltrated inflammatory, with linfocitos prevalence in glands exocrinas and knitted extraglandulares. The glandular lesion is characterized by the hiposecreción in mucous oral and ocular.  Clinical case:  a 13-year-old female adolescent with Sjögren's Syndrome is presented, whose initial clinical manifestation was extra-glandular, with the kidney as the main affected organ in type-I distal renal tubular acidosis.  Conclusions:  it is demonstrated that the realization of a meticulous anamnesis, clinical exploration and the use of different diagnostic tools, they make possible a precocious diagnosis of the illness and of their manifestations extraglandulares.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[SÍNDROME DE SJÖGREN, ACIDOSIS TUBULAR RENAL]]></kwd>
<kwd lng="es"><![CDATA[LINFOCITOS]]></kwd>
<kwd lng="es"><![CDATA[GLÁNDULAS EXOCRINAS]]></kwd>
<kwd lng="es"><![CDATA[PACIENTE]]></kwd>
<kwd lng="en"><![CDATA[SJOGREN'S SYNDROME, ACIDOSIS, RENAL TUBULAR]]></kwd>
<kwd lng="en"><![CDATA[LYMPHOCYTES]]></kwd>
<kwd lng="en"><![CDATA[EXOCRINE GLANDS]]></kwd>
<kwd lng="en"><![CDATA[PATIENT]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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