<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1561-3194</journal-id>
<journal-title><![CDATA[Revista de Ciencias Médicas de Pinar del Río]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Ciencias Médicas]]></abbrev-journal-title>
<issn>1561-3194</issn>
<publisher>
<publisher-name><![CDATA[Editorial Ciencias Médicas]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1561-31942022000500011</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Caracterización de la enfermedad de Creutzfeldt-Jakob en el Instituto Nacional de Neurología y Neurocirugía en La Habana]]></article-title>
<article-title xml:lang="en"><![CDATA[Characterization of Creutzfeldt-Jakob Disease at the National Institute of Neurology and Neurosurgery. Havana, Cuba]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Zayas-Fundora]]></surname>
<given-names><![CDATA[Emmanuel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Salgado-Fuentes]]></surname>
<given-names><![CDATA[Carlos Enrique]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Afonso-Domínguez]]></surname>
<given-names><![CDATA[María Karla]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Machado-Cueto]]></surname>
<given-names><![CDATA[María Fernanda]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Yllodo-Cristo]]></surname>
<given-names><![CDATA[Adriana]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Leyva-Pupo]]></surname>
<given-names><![CDATA[Liliana Virgen]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad de Ciencias Médicas de la Habana Facultad de Ciencias Médicas &#8216;&#8217;Manuel Fajardo&#8217;&#8217; ]]></institution>
<addr-line><![CDATA[La Habana ]]></addr-line>
<country>Cuba</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidad de Ciencias Médicas de Guantánamo. Hospital General Docente Octavio de la Concepción y de la Pedraja ]]></institution>
<addr-line><![CDATA[Guantánamo ]]></addr-line>
<country>Cuba</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>10</month>
<year>2022</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>10</month>
<year>2022</year>
</pub-date>
<volume>26</volume>
<numero>5</numero>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_arttext&amp;pid=S1561-31942022000500011&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_abstract&amp;pid=S1561-31942022000500011&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_pdf&amp;pid=S1561-31942022000500011&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN  Introducción:  la enfermedad de Creutzfeldt-Jakob (CJD) es un trastorno neurodegenerativo causado por priones en humanos. Se presenta como encefalopatía espongiforme de distribución mundial con una prevalencia de 1 cada 1 000 000 habitantes.  Objetivo:  caracterizar la enfermedad de Creutzfeldt-Jakob en el Instituto Nacional de Neurología y Neurocirugía durante el periodo de febrero 1981 a enero 2019.  Métodos:  se realizó un estudio observacional, descriptivo transversal, en pacientes diagnosticados con enfermedad de Creutzfeldt-Jakob, de etiología no hereditaria, en el Instituto Nacional de Neurología y Neurocirugía de Cuba, entre 1981 y 2019. El universo estuvo constituido por los 12 pacientes diagnosticados en dicho periodo.  Resultados:  predominó el sexo femenino para un 66,3 %. La estadía hospitalaria media fue de 9,8 días para un mínimo de siete y un máximo de 46 días. El primer síntoma identificado por el paciente fue la dificultad para caminar, seguido de la pérdida del equilibrio y los mareos. El hallazgo radiológico predominante fue la atrofia frontoparieto temporal y cerebelosa en el 50 % de los pacientes. Las manifestaciones clínicas más frecuentes fueron la afasia, desorientación, disartria, disfagia y los trastornos de la micción en la misma proporción.  Conclusiones:  en la investigación se observó un mayor número de casos del sexo femenino. La dificultad para caminar seguido de la pérdida del equilibrio y los mareos fueron los primeros síntomas identificados. Predominó como hallazgo radiológico la atrofia frontoparietotemporal y cerebelosa. Las manifestaciones clínicas más frecuentes fueron la afasia, desorientación, disartria, disfagia y los trastornos de la micción.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ ABSTRACT  Introduction:  Creutzfeldt-Jakob disease (CJD) is a neurodegenerative disorder caused by prions in humans. It presents as a spongiform encephalopathy of worldwide distribution with a prevalence of 1 in 1,000,000 inhabitants.  Objective:  to characterize Creutzfeldt-Jakob disease at the National Institute of Neurology and Neurosurgery during the period from February 1981 to January 2019.  Methods:  an observational, descriptive cross-sectional study was carried out on patients diagnosed with Creutzfeldt-Jakob disease, of non-hereditary etiology, at the National Institute of Neurology and Neurosurgery of Cuba between 1981 and 2019. The universe was constituted by the 12 patients diagnosed in that period.  Results:  female sex predominated in 66,3 %. The mean hospital stay was 9,8 days with a minimum of 7 and a maximum of 46 days. The first symptom identified by the patient was difficulty walking (50 %), followed by loss of balance (33 %) and dizziness (17 %). The predominant radiological finding was frontoparietotemporal and cerebellar atrophy in 50 % of patients. The most frequent clinical manifestations were aphasia in 25 %, disorientation, dysarthria, dysphagia and urination disorders in the same proportion.  Conclusions:  In the investigation a greater number of cases were observed in the female sex. Difficulty walking followed by loss of balance and dizziness were the first symptoms identified. Frontoparietotemporal and cerebellar atrophy predominated as radiological findings. The most frequent clinical manifestations were aphasia, disorientation, dysarthria, dysphagia and urination disorders.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[ENFERMEDADES NEURODEGENERATIVAS]]></kwd>
<kwd lng="es"><![CDATA[PRIONES]]></kwd>
<kwd lng="es"><![CDATA[SÍNDROME DE CREUTZFELDT-JAKOB]]></kwd>
<kwd lng="es"><![CDATA[ENCEFALOPATÍA ESPONGIFORME]]></kwd>
<kwd lng="en"><![CDATA[NEURODEGENERATIVE DISEASES]]></kwd>
<kwd lng="en"><![CDATA[PRIONS]]></kwd>
<kwd lng="en"><![CDATA[CREUTZFELDT-JAKOB SYNDROME]]></kwd>
<kwd lng="en"><![CDATA[ENCEPHALOPATHY, SPONGIFORM]]></kwd>
</kwd-group>
</article-meta>
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