<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1726-6718</journal-id>
<journal-title><![CDATA[Revista Cubana de Anestesiología y Reanimación]]></journal-title>
<abbrev-journal-title><![CDATA[Rev cuba anestesiol reanim]]></abbrev-journal-title>
<issn>1726-6718</issn>
<publisher>
<publisher-name><![CDATA[Editorial Ciencias Médicas]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1726-67182022000300002</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Anestesia en una paciente con angioedema hereditario]]></article-title>
<article-title xml:lang="en"><![CDATA[Anesthesia in a patient with hereditary angioedema]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Fernández Montoya]]></surname>
<given-names><![CDATA[Carlos Enrique]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Redondo Gómez]]></surname>
<given-names><![CDATA[Zhachel Alejandro]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[García García]]></surname>
<given-names><![CDATA[Dayné]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital &#8220;Dr. Gustavo Aldereguía Lima&#8221;  ]]></institution>
<addr-line><![CDATA[ Cienfuegos]]></addr-line>
<country>Cuba</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Instituto Nacional de Oncología y Radiobiología  ]]></institution>
<addr-line><![CDATA[ La Habana]]></addr-line>
<country>Cuba</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2022</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2022</year>
</pub-date>
<volume>21</volume>
<numero>3</numero>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_arttext&amp;pid=S1726-67182022000300002&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_abstract&amp;pid=S1726-67182022000300002&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_pdf&amp;pid=S1726-67182022000300002&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN El angioedema hereditario (AEH) es una enfermedad genética poco frecuente debida a una mutación de transmisión autosómica dominante que produce una alteración del gen que codifica la proteína inhibidora de la C1 esterasa activada (C1-INH), provoca un déficit o disfunción de la misma. Se caracteriza por episodios recurrentes y autolimitados con síntomas transitorios de hinchazón sin urticaria de tejidos subcutáneos, extremidades, pared intestinal, genitales y vías respiratorias superiores. La afectación de laringe y glotis puede ocasionar la muerte por asfixia. Se informa la conducción perioperatoria en una paciente portadora de AEH y un amplio historial de alergias donde las principales consideraciones están relacionadas con la prevención de una crisis aguda durante el perioperatorio. Para lograrlo se requirió de una preparación con plasma fresco congelado (PFC) y ácido tranexámico (ATX) con días de antelación a la cirugía que se continuó en el posoperatorio, además de un manejo cuidadoso durante el acto anestésico.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT Hereditary angioedema (HAE) is a rare genetic disease caused by an autosomal dominant mutation that results in an alteration of the gene encoding the activated C1 esterase inhibitor protein (C1-INH), causing deficiency or dysfunction of C1-INH. It is characterized by recurrent and self-limited episodes with transient symptoms of swelling without urticaria of subcutaneous tissues, extremities, intestinal wall, genitalia and upper respiratory tract. Involvement of the larynx and glottis may result in death by asphyxia. The perioperative managment is reported of a patient with HAE and a long history of allergies in which the main considerations are related to the prevention of an acute crisis during the perioperative period. This required a preparation with fresh frozen plasma and tranexamic acid days before surgery, which was continued postoperatively, in addition to careful management during the anesthetic procedure.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[angioedema hereditario]]></kwd>
<kwd lng="es"><![CDATA[deficiencia de C1-INH]]></kwd>
<kwd lng="es"><![CDATA[anestesia]]></kwd>
<kwd lng="en"><![CDATA[hereditary angioedema]]></kwd>
<kwd lng="en"><![CDATA[C1-INH deficiency]]></kwd>
<kwd lng="en"><![CDATA[anesthesia]]></kwd>
</kwd-group>
</article-meta>
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