<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2078-7170</journal-id>
<journal-title><![CDATA[CorSalud]]></journal-title>
<abbrev-journal-title><![CDATA[CorSalud]]></abbrev-journal-title>
<issn>2078-7170</issn>
<publisher>
<publisher-name><![CDATA[Cardiocentro Ernesto Che Guevara]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2078-71702020000100093</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Torsión de puntas en una paciente con síndrome de QT largo congénito durante el puerperio: Presentación de un caso]]></article-title>
<article-title xml:lang="en"><![CDATA[Torsades de pointes in a patient with congenital long QT syndrome during the puerperium: Case report]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Ravelo Dopico]]></surname>
<given-names><![CDATA[Roger]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Silva Gutiérrez]]></surname>
<given-names><![CDATA[Máximo L.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Medina Rivero]]></surname>
<given-names><![CDATA[Gerardo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Cruz Rodríguez]]></surname>
<given-names><![CDATA[Liz O.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Cárdenas Fernández]]></surname>
<given-names><![CDATA[Yoanis]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Yunez Saab]]></surname>
<given-names><![CDATA[Pedro]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Valdés Carrazana]]></surname>
<given-names><![CDATA[Eliset]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Militar Central Dr. Carlos J. Finlay Servicio de Cardiología ]]></institution>
<addr-line><![CDATA[Marianao La Habana]]></addr-line>
<country>Cuba</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>03</month>
<year>2020</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>03</month>
<year>2020</year>
</pub-date>
<volume>12</volume>
<numero>1</numero>
<fpage>93</fpage>
<lpage>98</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_arttext&amp;pid=S2078-71702020000100093&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_abstract&amp;pid=S2078-71702020000100093&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_pdf&amp;pid=S2078-71702020000100093&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN El síndrome de QT largo congénito es una enfermedad eléctrica primaria del corazón que predispone a la ocurrencia de arritmias ventriculares malignas. Se traduce en una prolongación del intervalo QT en el electrocardiograma y la torsión de puntas es la arritmia que ocasiona síncope y, en ocasiones, muerte súbita. El embarazo y el puerperio aumentan la incidencia de estos eventos. Se presenta el caso de una puérpera afectada que presentó crisis de ansiedad y desmayos interpretados como psicógenos. Se documentó torsión de puntas sin respuesta a los fármacos antiarrítmicos diponibles y se trasladó al centro de referencia (Instituto de Cardiología y Cirugía Cardiovascular), donde se aumentó la frecuencia de estimulación del marcapasos y, posteriormente, se implantó un desfibrilador automático. Se trata de un caso infrecuente que constituyó un verdadero reto en el tratamiento integral y emergente, todo lo cual posibilitó la supervivencia de la paciente.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT Congenital long QT syndrome is a primary electrical disorder of the heart which predisposes to the occurrence of malignant ventricular arrhythmias. It is characterized by a prolongation of the QT interval on the electrocardiogram and the torsade de pointes is the main associated arrhythmia, resulting in syncope and sudden cardiac death. Pregnancy and puerperium increase the incidence of those events. We present the case of a patient who suffered from this disorder, and during the post-delivery period, she had events of faint and anxiety interpreted as psychogenic. Torsades de pointes without response to the available antiarrhythmic drugs was documented and she was transferred to the reference center (Instituto de Cardiología y Cirugía Cardiovascular), where the pacemaker stimulation frequency was increased and, subsequently, an implantable cardioverter defibrillator was implanted. This is an infrequent case that was a real challenge for the comprehensive and emergent treatment, all of which enabled the survival of the patient.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Síndrome de QT largo congénito]]></kwd>
<kwd lng="es"><![CDATA[Torsión de puntas]]></kwd>
<kwd lng="es"><![CDATA[Muerte súbita cardíaca]]></kwd>
<kwd lng="es"><![CDATA[Puerperio]]></kwd>
<kwd lng="en"><![CDATA[Congenital long QT syndrome]]></kwd>
<kwd lng="en"><![CDATA[Torsades de pointes]]></kwd>
<kwd lng="en"><![CDATA[Sudden cardiac death]]></kwd>
<kwd lng="en"><![CDATA[Puerperium]]></kwd>
</kwd-group>
</article-meta>
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