<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2709-7927</journal-id>
<journal-title><![CDATA[Acta Médica del Centro]]></journal-title>
<abbrev-journal-title><![CDATA[Acta méd centro]]></abbrev-journal-title>
<issn>2709-7927</issn>
<publisher>
<publisher-name><![CDATA[Hospital Provincial Clínico Quirúrgico Universitario Arnaldo Milián Castro]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2709-79272023000100161</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Manejo anestésico de pacientes con ataxia espinocerebelosa tipo 2. A propósito de un caso]]></article-title>
<article-title xml:lang="en"><![CDATA[Anesthetic management of patients with spinocerebellar ataxia type 2. A case report]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rodríguez Calderón]]></surname>
<given-names><![CDATA[Alina]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Nieto Monteagudo]]></surname>
<given-names><![CDATA[Carlos Gilberto]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Nieto Martínez]]></surname>
<given-names><![CDATA[Gretter Elena]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Provincial Clínico Quirúrgico Universitario &#8220;Arnaldo Milián Castro&#8221;  ]]></institution>
<addr-line><![CDATA[Santa Clara Villa Clara]]></addr-line>
<country>Cuba</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Hospital Universitario &#8220;Celestino Hernández Robau&#8221;  ]]></institution>
<addr-line><![CDATA[Santa Clara Villa Clara]]></addr-line>
<country>Cuba</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>03</month>
<year>2023</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>03</month>
<year>2023</year>
</pub-date>
<volume>17</volume>
<numero>1</numero>
<fpage>161</fpage>
<lpage>167</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_arttext&amp;pid=S2709-79272023000100161&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_abstract&amp;pid=S2709-79272023000100161&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_pdf&amp;pid=S2709-79272023000100161&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN  Introducción:  la ataxia espinocerebelosa tipo 2 es una enfermedad hereditaria con carácter autosómico dominante en la que se produce degeneración del cerebelo y sus vías aferentes y eferentes y que se caracteriza por ataxia, disartria, dismetría, adiadococinesia, temblor de acción, contracturas musculares dolorosas, neuropatía precoz, nistagmos, signos piramidales y trastornos cognitivos, del sueño y autonómicos.  Información del paciente:  se informa el manejo anestésico en un paciente en el que las principales implicaciones de la anestesia están relacionadas con la degeneración neuromuscular y la posible aparición de complicaciones respiratorias.  Conclusiones:  la selección adecuada de los agentes anestésicos, el uso de relajantes musculares no despolarizantes en dosis reducidas, la anestesia epidural combinada con anestesia general, la retirada precoz del tubo endotraqueal o máscara laríngea, la movilización precoz y la monitorización neuromuscular y cardiorespiratoria son los elementos fundamentales en el manejo anestésico de este paciente.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT  Introduction:  spinocerebellar ataxia type 2 is an autosomal dominant inherited disease in which degeneration of the cerebellum and its afferent and efferent pathways occurs and is characterized by ataxia, dysarthria, dysmetria, adiadochokinesia, action tremor, painful muscle contractures, early neuropathy, nystagmus, pyramidal signs, and cognitive, sleep and autonomic disorders.  Patient information:  anesthetic management is reported in a patient in which the main implications of anesthesia are related to neuromuscular degeneration and the possible occurrence of respiratory complications.  Conclusions:  the adequate selection of anesthetic agents, the use of non-depolarizing muscle relaxants in reduced doses, epidural anesthesia combined with general anesthesia, early removal of the endotracheal tube or laryngeal mask, early mobilization and neuromuscular and cardiorespiratory monitoring are the fundamental elements in the anesthetic management of this patient.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[ataxia espinocerebelosa]]></kwd>
<kwd lng="es"><![CDATA[manejo anestésico]]></kwd>
<kwd lng="es"><![CDATA[monitoreo]]></kwd>
<kwd lng="en"><![CDATA[spinocerebellar ataxia]]></kwd>
<kwd lng="en"><![CDATA[anesthetic management]]></kwd>
<kwd lng="en"><![CDATA[monitoring]]></kwd>
</kwd-group>
</article-meta>
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