<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0864-0289</journal-id>
<journal-title><![CDATA[Revista Cubana de Hematología, Inmunología y Hemoterapia]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Cubana Hematol Inmunol Hemoter]]></abbrev-journal-title>
<issn>0864-0289</issn>
<publisher>
<publisher-name><![CDATA[Centro Nacional de Información de Ciencias MédicasEditorial Ciencias Médicas]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0864-02892023000100004</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Enfermedades autoinmunes asociadas a inmunodeficiencias primarias]]></article-title>
<article-title xml:lang="en"><![CDATA[Autoimmune diseases associated with primary immunodeficiencies]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[González-Costa]]></surname>
<given-names><![CDATA[Maricarmen]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Addine Ramírez]]></surname>
<given-names><![CDATA[Bárbara de la Caridad]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Pérez Acevedo]]></surname>
<given-names><![CDATA[Lidia Cecilia]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Viamonte Piña]]></surname>
<given-names><![CDATA[Vanesa]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Figueredo Santos]]></surname>
<given-names><![CDATA[Onailimizan]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Marrón González]]></surname>
<given-names><![CDATA[Reynel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Provincial Pediátrico Docente General Milanés Facultad de Ciencias Médicas de Bayamo ]]></institution>
<addr-line><![CDATA[ Granma]]></addr-line>
<country>Cuba</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Facultad de Ciencias Médicas de Bayamo  ]]></institution>
<addr-line><![CDATA[ Granma]]></addr-line>
<country>Cuba</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Hospital Provincial Universitario Carlos Manuel de Céspedes Facultad de Ciencias Médicas de Bayamo ]]></institution>
<addr-line><![CDATA[ Granma]]></addr-line>
<country>Cuba</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>00</month>
<year>2023</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>00</month>
<year>2023</year>
</pub-date>
<volume>39</volume>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_arttext&amp;pid=S0864-02892023000100004&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_abstract&amp;pid=S0864-02892023000100004&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_pdf&amp;pid=S0864-02892023000100004&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN  Introducción:  Las enfermedades y manifestaciones autoinmunes ocupan el segundo lugar de las enfermedades por inmunodeficiencia primaria, después de las infecciones.  Objetivo: Determinar el comportamiento de las enfermedades autoinmunes en los pacientes con inmunodeficiencias primarias.  Métodos:  Se realizó estudio de caso control en el servicio de Alergia e Inmunología de Bayamo, Granma entre los años 2013 y 2022. El grupo de estudio fue de 38 pacientes con diagnóstico de inmunodeficiencia primaria y el grupo control de 76 pacientes sin compromiso del sistema inmune. Se empleó el programa estadístico SPSS 25, las frecuencias absolutas y relativas, odds ratio y Chi cuadrado.  Resultados: Las manifestaciones sugerentes de autoinmunidad en los pacientes con inmunodeficiencias primarias fue 39,47 % y en los controles 3,95 %, OR = 15,869 y p= 0,000. Las más frecuentes fueron: dolor monoarticular en 6 pacientes (33,33 %); poliartralgia, dermatitis y alopecia en 3 casos (16,67 %) cada uno; dolor en la columna vertebral y nódulos subcutáneos, un paciente (5,56 %) cada uno. Las enfermedades autoinmunes asociadas a inmunodeficiencias primarias fueron: enfermedad celiaca (30,71 %), vitíligo (23,07 %), fibromialgia (15,38 %), eritema nodoso, la gastritis eosinofílica, anemia perniciosa y vasculitis con 7,69 % cada uno.  Conclusiones:  Las manifestaciones y enfermedades autoinmunes prevalecieron en pacientes con inmunodeficiencias primarias; en ambos casos fueron más frecuentes en los pacientes mayores de 18 años de edad. Las inmunodeficiencias más frecuentemente asociadas a los trastornos autoinmunes fueron las deficiencias predominantemente de anticuerpos y los defectos desregulatorios.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT  Introduction:  Autoimmune diseases are in second place, after infections to suspect primary immunodeficiency diseases.  Objective:  To determine the behavior of autoimmune diseases in patients with primary immunodeficiencies.  Methods:  A case control study was carried out in the allergy and immunology service of Bayamo, Granma between 2013 and 2022. The universe was studied as a whole, the study group with 38 patients diagnosed with primary immunodeficiency and the control group with 76 patients without immune system compromise. The SPSS 25 statistical program, absolute and relative frequencies, odds ratio and chi-square were used.  Results:  The manifestations suggestive of autoimmunity in patients with PID was 39.47% and in controls 3.95%, OR = 15.869 and p = 0.000 and the most frequent were: monoarticular pain in 6 patients (33.33%), polyarthralgia, dermatitis and alopecia with 3 cases (16.67%) each one, pain in dorsal spine and subcutaneous nodule, one patient (5.56%) each one. Immune diseases associated with PID were: celiac disease (30.71%), vitiligo (23.07%), fibromyalgia (15.38%), erythema nodosum, eosinophilic gastritis, pernicious anemia and vasculitis with 7.69% each.  Conclusions:  Autoimmune manifestations and diseases prevailed in patients with PID, in both cases were more frequent in patients older than 18 years. The immunodeficiencies most frequently associated with autoimmune disorders were those of antibodies and those with some dysregulation component.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[enfermedades autoinmunes]]></kwd>
<kwd lng="es"><![CDATA[autoinmunidad]]></kwd>
<kwd lng="es"><![CDATA[inmunodeficiencias primarias]]></kwd>
<kwd lng="es"><![CDATA[enfermedad celiaca]]></kwd>
<kwd lng="es"><![CDATA[IPEX-like]]></kwd>
<kwd lng="es"><![CDATA[inmunodeficiencia por desregulación]]></kwd>
<kwd lng="en"><![CDATA[autoimmunity]]></kwd>
<kwd lng="en"><![CDATA[primary immunodeficiencies]]></kwd>
<kwd lng="en"><![CDATA[celiac disease]]></kwd>
<kwd lng="en"><![CDATA[IPEX like]]></kwd>
<kwd lng="en"><![CDATA[dysregulation immunodeficiency]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<label>1</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Llobell]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Español]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Mensa-Vilaro]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Esteve]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Ruiz]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
<name>
<surname><![CDATA[González-Navarro]]></surname>
<given-names><![CDATA[EA]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[From Primary Immunodeficiency to Autoimmunity How Extreme Situations Highlight the Main Genetic Factors Involved in Autoimmune Disease]]></article-title>
<source><![CDATA[MOJ Immunol]]></source>
<year>2016</year>
<volume>4</volume>
<numero>1</numero>
<issue>1</issue>
</nlm-citation>
</ref>
<ref id="B2">
<label>2</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Casado Hernández]]></surname>
<given-names><![CDATA[I]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Inmunodeficiencias primarias y citopenias]]></article-title>
<source><![CDATA[Rev Cubana Hematol Inmunol Hemoter]]></source>
<year>2019</year>
<volume>35</volume>
<numero>4</numero>
<issue>4</issue>
</nlm-citation>
</ref>
<ref id="B3">
<label>3</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Bousfiha]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Jeddane]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Picard]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
<name>
<surname><![CDATA[Al-Herz]]></surname>
<given-names><![CDATA[W]]></given-names>
</name>
<name>
<surname><![CDATA[Ailal]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
<name>
<surname><![CDATA[Chatila]]></surname>
<given-names><![CDATA[T]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Human Inborn Errors of Immunity 2019 Update of the IUIS Phenotypical Classification]]></article-title>
<source><![CDATA[J Clin Immunol]]></source>
<year>2020</year>
<volume>40</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>66-81</page-range></nlm-citation>
</ref>
<ref id="B4">
<label>4</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Condino-Neto]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Sorensen]]></surname>
<given-names><![CDATA[RU]]></given-names>
</name>
<name>
<surname><![CDATA[Gómez Raccio]]></surname>
<given-names><![CDATA[AC]]></given-names>
</name>
<name>
<surname><![CDATA[King]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Espinosa-Rosales]]></surname>
<given-names><![CDATA[FJ]]></given-names>
</name>
<name>
<surname><![CDATA[Franco]]></surname>
<given-names><![CDATA[JL]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Current state and future perspectives of the Latin American Society for Immunodeficiencies (LASID)]]></article-title>
<source><![CDATA[Allergol Immunopathol]]></source>
<year>2015</year>
<volume>43</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>493-7</page-range></nlm-citation>
</ref>
<ref id="B5">
<label>5</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Macías]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Una mirada al diagnóstico y tratamiento de las inmunodeficiencias primarias en Cuba]]></article-title>
<source><![CDATA[Rev Cubana Hematol Inmunol Hemoter]]></source>
<year>2019</year>
<volume>35</volume>
<numero>4</numero>
<issue>4</issue>
</nlm-citation>
</ref>
<ref id="B6">
<label>6</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Fischer]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Provot]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Jais]]></surname>
<given-names><![CDATA[JP]]></given-names>
</name>
<name>
<surname><![CDATA[Alcais]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Autoimmune and inflammatory manifestations occur frequently in patients with primary immunodeficiencies]]></article-title>
<source><![CDATA[J Allergy Clin Immunol]]></source>
<year>2017</year>
<volume>140</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>1388-93.e8</page-range></nlm-citation>
</ref>
<ref id="B7">
<label>7</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Serpa-Almaguer]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Chall-Rodríguez]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Enfermedades autoinmunes en niños con diagnóstico de inmunodeficiencias primarias]]></article-title>
<source><![CDATA[Rev Cubana Hematol Inmunol Hemoter]]></source>
<year>2017</year>
<volume>36</volume>
<numero>^sSupl</numero>
<issue>^sSupl</issue>
<supplement>Supl</supplement>
</nlm-citation>
</ref>
<ref id="B8">
<label>8</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Solé]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Primary immunodeficiencies a diagnostic challenge?]]></article-title>
<source><![CDATA[J. Pediatr. (Rio J.) 2021]]></source>
<year>2021</year>
<volume>97</volume>
<numero>^sSuppl</numero>
<issue>^sSuppl</issue>
<supplement>Suppl</supplement>
<page-range>S1-2</page-range></nlm-citation>
</ref>
<ref id="B9">
<label>9</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Odnoletkova]]></surname>
<given-names><![CDATA[I]]></given-names>
</name>
<name>
<surname><![CDATA[Kindle]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Quinti]]></surname>
<given-names><![CDATA[I]]></given-names>
</name>
<name>
<surname><![CDATA[Grimbacher]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
<name>
<surname><![CDATA[Knerr]]></surname>
<given-names><![CDATA[V]]></given-names>
</name>
</person-group>
<collab>Plasma Protein Therapeutics Association Taskforce</collab>
<article-title xml:lang=""><![CDATA[The burden of common variable immunodeficiency disorders a retrospective analysis of the European Society for Immunodeficiency (ESID) registry data]]></article-title>
<source><![CDATA[Orphanet J Rare Dis]]></source>
<year>2018</year>
<volume>13</volume>
<numero>1</numero>
<issue>1</issue>
</nlm-citation>
</ref>
<ref id="B10">
<label>10</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Agarwal]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Cunningham-Rundles]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Autoimmunity in common variable immunodeficiency]]></article-title>
<source><![CDATA[Ann Allergy Asthma Immunol]]></source>
<year>2019</year>
<volume>123</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>454-60</page-range></nlm-citation>
</ref>
<ref id="B11">
<label>11</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Berrón-Ruiz]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Enfermedades autoimunitarias en pacientes con inmunodeficiencia común variable]]></article-title>
<source><![CDATA[Rev Alerg Mex]]></source>
<year>2021</year>
<volume>6</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>48-64</page-range></nlm-citation>
</ref>
<ref id="B12">
<label>12</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Huang]]></surname>
<given-names><![CDATA[Q]]></given-names>
</name>
<name>
<surname><![CDATA[Liu]]></surname>
<given-names><![CDATA[X]]></given-names>
</name>
<name>
<surname><![CDATA[Zhang]]></surname>
<given-names><![CDATA[Y]]></given-names>
</name>
<name>
<surname><![CDATA[Huang]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Li]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Li]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Molecular feature and therapeutic perspectives of immune dysregulation, polyendocrinopathy, enteropathy, X-linked syndrome]]></article-title>
<source><![CDATA[J Genet Genomics]]></source>
<year>2020</year>
<volume>47</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>17-26</page-range></nlm-citation>
</ref>
<ref id="B13">
<label>13</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Caldirola]]></surname>
<given-names><![CDATA[MS]]></given-names>
</name>
<name>
<surname><![CDATA[Martínez]]></surname>
<given-names><![CDATA[MP]]></given-names>
</name>
<name>
<surname><![CDATA[Bezrodnik]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Zwirner]]></surname>
<given-names><![CDATA[NW]]></given-names>
</name>
<name>
<surname><![CDATA[Gaillard]]></surname>
<given-names><![CDATA[MI]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Immune Monitoring of Patients With Primary Immune Regulation Disorders Unravels Higher Frequencies of Follicular T Cells with different pro? les that associate with alterations in B Cell subsets]]></article-title>
<source><![CDATA[Front. Immunol]]></source>
<year>2020</year>
<volume>11</volume>
</nlm-citation>
</ref>
<ref id="B14">
<label>14</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Bezrodnik]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Di Giovanni]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Caldirola]]></surname>
<given-names><![CDATA[MS]]></given-names>
</name>
<name>
<surname><![CDATA[Azcoiti]]></surname>
<given-names><![CDATA[ME]]></given-names>
</name>
<name>
<surname><![CDATA[Torgerson]]></surname>
<given-names><![CDATA[T]]></given-names>
</name>
<name>
<surname><![CDATA[Gaillard]]></surname>
<given-names><![CDATA[MI]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Long-Term Follow-up of STAT5B Deficiency in Three Argentinian Patients Clinical and Immunological Features]]></article-title>
<source><![CDATA[J Clin Immunol]]></source>
<year>2015</year>
<volume>35</volume>
<page-range>264-72</page-range></nlm-citation>
</ref>
<ref id="B15">
<label>15</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Bonilla]]></surname>
<given-names><![CDATA[FA]]></given-names>
</name>
<name>
<surname><![CDATA[Barlan]]></surname>
<given-names><![CDATA[I]]></given-names>
</name>
<name>
<surname><![CDATA[Chapel]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
<name>
<surname><![CDATA[Costa-Carvalho]]></surname>
<given-names><![CDATA[BT]]></given-names>
</name>
<name>
<surname><![CDATA[Cunningham-Rundles]]></surname>
<given-names><![CDATA[CH]]></given-names>
</name>
<name>
<surname><![CDATA[de la Morena]]></surname>
<given-names><![CDATA[MT]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[International Consensus Document (ICON): Common Variable Immunodeficiency Disorders]]></article-title>
<source><![CDATA[J Allergy Clin Immunol Pract]]></source>
<year>2016</year>
<volume>4</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>38-59</page-range></nlm-citation>
</ref>
<ref id="B16">
<label>16</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Abolhassani]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
<name>
<surname><![CDATA[Gharib]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
<name>
<surname><![CDATA[Shahinpour]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Masoom]]></surname>
<given-names><![CDATA[SN]]></given-names>
</name>
<name>
<surname><![CDATA[Havaei]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Mirminachi]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Autoimmunity in patients with selective IgA deficiency]]></article-title>
<source><![CDATA[J Investig Allergol Clin Immunol]]></source>
<year>2015</year>
<volume>25</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>112-9</page-range></nlm-citation>
</ref>
<ref id="B17">
<label>17</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Domínguez]]></surname>
<given-names><![CDATA[O]]></given-names>
</name>
<name>
<surname><![CDATA[Giner]]></surname>
<given-names><![CDATA[MT]]></given-names>
</name>
<name>
<surname><![CDATA[Alsina]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Martín]]></surname>
<given-names><![CDATA[MA]]></given-names>
</name>
<name>
<surname><![CDATA[Lozano]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Plaza]]></surname>
<given-names><![CDATA[AM]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Fenotipos clínicos asociados a la deficiencia selectiva de IgA revisión de 330 casos y propuesta de un protocolo de seguimiento]]></article-title>
<source><![CDATA[An Pediatría]]></source>
<year>2012</year>
<volume>76</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>261-7</page-range></nlm-citation>
</ref>
<ref id="B18">
<label>18</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Megna]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Pecoraro]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Balato]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
<name>
<surname><![CDATA[Villani]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Crescenzi]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Balato]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Psoriasis in a cohort of patients with common variable immunodeficiency]]></article-title>
<source><![CDATA[Br J Dermatol]]></source>
<year>2019</year>
<volume>180</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>935-6</page-range></nlm-citation>
</ref>
<ref id="B19">
<label>19</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Crowley]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
<name>
<surname><![CDATA[Ruffner]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[McDonald McGinn]]></surname>
<given-names><![CDATA[DM]]></given-names>
</name>
<name>
<surname><![CDATA[Sullivan]]></surname>
<given-names><![CDATA[KE]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Variable immune deficiency related to delection size in chromosome 22q11 2 delection syndrome]]></article-title>
<source><![CDATA[Am J Med Genet A]]></source>
<year>2018</year>
<volume>176</volume>
<page-range>2082-6</page-range></nlm-citation>
</ref>
<ref id="B20">
<label>20</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Walter]]></surname>
<given-names><![CDATA[JE]]></given-names>
</name>
<name>
<surname><![CDATA[Ayala]]></surname>
<given-names><![CDATA[IA]]></given-names>
</name>
<name>
<surname><![CDATA[Milojevic]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Autoimmunity as a continuum in primary immunodeficiency]]></article-title>
<source><![CDATA[Curr Opin Pediatr]]></source>
<year>2019</year>
<volume>31</volume>
<numero>6</numero>
<issue>6</issue>
<page-range>851-62</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
