<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1561-3194</journal-id>
<journal-title><![CDATA[Revista de Ciencias Médicas de Pinar del Río]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Ciencias Médicas]]></abbrev-journal-title>
<issn>1561-3194</issn>
<publisher>
<publisher-name><![CDATA[Editorial Ciencias Médicas]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1561-31942020000400016</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Ictiosis lamelar en una unidad neonatal]]></article-title>
<article-title xml:lang="en"><![CDATA[Lamellar Ichthyosis: a case study in a neonatal unit]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Vázquez Gutiérrez]]></surname>
<given-names><![CDATA[Giselle Lucila]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Granados Perez]]></surname>
<given-names><![CDATA[Gabriel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[de la Rosa Santana]]></surname>
<given-names><![CDATA[Jesús Daniel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad de Ciencias Médicas de Granma Dirección de Ciencia e Innovación Tecnológica ]]></institution>
<addr-line><![CDATA[Manzanillo Granma]]></addr-line>
<country>Cuba</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidad de Ciencias Médicas de Granma Hospital Provincial Ginecobstétrico Fe del Valle Ramos. Manzanillo ]]></institution>
<addr-line><![CDATA[Granma ]]></addr-line>
<country>Cuba</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Universidad de Ciencias Médicas de Granma Facultad de Ciencias Médicas Celia Sánchez Manduley. Manzanillo ]]></institution>
<addr-line><![CDATA[Granma ]]></addr-line>
<country>Cuba</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>08</month>
<year>2020</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>08</month>
<year>2020</year>
</pub-date>
<volume>24</volume>
<numero>4</numero>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_arttext&amp;pid=S1561-31942020000400016&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_abstract&amp;pid=S1561-31942020000400016&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_pdf&amp;pid=S1561-31942020000400016&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN  Introducción:  en el recién nacido pueden ser evidentes numerosos trastornos hereditarios, que causan afectaciones en la pigmentación, textura, elasticidad e integridad estructural del tegumento. La ictiosis laminar o eritrodermiaictiosiforme congénita es una genodermatosis autosómica recesiva poco frecuente, caracterizada por un cuadro eritrodérmico, queratodermia palmo-plantar, onicosis y otros trastornos.  Presentación del caso:  recién nacido con ictiosis lamelar, hospitalizado en la unidad de cuidados intensivos neonatal del hospital Ginecobstétrico Fe del Valle Ramos, en el municipio de Manzanillo. El tratamiento se centró en mantener la entereza de la piel mediante humectación y lubricación continua con emolientes, control de la temperatura, nutrición y prevención de infecciones secundarias.  Conclusiones:  se afirma que la atención multidisciplinaria y la implementación del plan de cuidados, fue esencial para el éxito del tratamiento. Hubo mejora de la piel y mucosas, prevención de infecciones. Se favorecieron las condiciones de supervivencia y autonomía de los padres para los cuidados en domicilio.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT  Introduction:  in the newborn, numerous hereditary disorders may be evident, which can cause various aberrations of pigmentation, texture, elasticity and structural integrity of the integument. Among these pathologies are ichthyosis, from the Greek ichthys which means fish. Laminar Ichthyosis or Congenital Ichthyosiform Erythroderma (CIE) is a rare autosomal recessive genodermatosis (1/300 000 births worldwide), characterized by an erythrodermic condition, palmoplantar keratoderma (PPK), onicosis, and other disorders.  Case report:  a newborn with Lamellar Ichthyosis hospitalized in the neonatal intensive care unit at Fe del Valle Ramos Gynecological Obstetric Hospital, in Manzanillo municipality, Granma province. Medical care was based on maintaining the integrity of the skin through moisturizing and continuous lubrication with emollients, temperature control, nutrition and prevention of secondary infections.  Conclusions:  through the case study, it is stated that the medical appointments with other specialties for the multidisciplinary care and the implementation of the care plan were essential regarding the multidisciplinary success of the treatment. There was improvement of the skin and mucosa, prevention of infections, concluding with favorable conditions of survival and autonomy of the parents for home care.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[ICTIOSIS LAMELAR]]></kwd>
<kwd lng="es"><![CDATA[ANOMALÍAS CONGÉNITAS]]></kwd>
<kwd lng="es"><![CDATA[QUERATODERMIA PALMOPLANTAR]]></kwd>
<kwd lng="en"><![CDATA[ICHTHYOSIS, LAMELLAR]]></kwd>
<kwd lng="en"><![CDATA[CONGENITAL ABNORMALITIES]]></kwd>
<kwd lng="en"><![CDATA[KERATODERMA, PALMOPLANTAR]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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