<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1817-5996</journal-id>
<journal-title><![CDATA[Revista Cubana de Reumatología]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Cuba Reumatol]]></abbrev-journal-title>
<issn>1817-5996</issn>
<publisher>
<publisher-name><![CDATA[Editorial CIMEQ]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1817-59962022000400002</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Características clínico-epidemiológicas de los pacientes con esclerosis sistémica]]></article-title>
<article-title xml:lang="en"><![CDATA[Clinical-epidemiological characteristics of patients with systemic sclerosis]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[López Mantecón]]></surname>
<given-names><![CDATA[Ana Marta]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rodríguez Echegoyen]]></surname>
<given-names><![CDATA[Dalgis Ruth]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Pozo Abreu]]></surname>
<given-names><![CDATA[Silvia María]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Mederos Castellanos]]></surname>
<given-names><![CDATA[Ailyn]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Domínguez García]]></surname>
<given-names><![CDATA[Jacqueline]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad de Ciencias Médicas de La Habana Centro de Referencia para las Enfermedades Reumáticas ]]></institution>
<addr-line><![CDATA[ La Habana]]></addr-line>
<country>Cuba</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidad de Ciencias Médicas de Ciego de Ávila Hospital General Dr. Antonio Luaces Iraola ]]></institution>
<addr-line><![CDATA[ La Habana]]></addr-line>
<country>Cuba</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Universidad de Ciencias Médicas de La Habana Hospital Docente Clínico Quirúrgico 10 de Octubre ]]></institution>
<addr-line><![CDATA[ La Habana]]></addr-line>
<country>Cuba</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2022</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2022</year>
</pub-date>
<volume>24</volume>
<numero>4</numero>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_arttext&amp;pid=S1817-59962022000400002&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_abstract&amp;pid=S1817-59962022000400002&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_pdf&amp;pid=S1817-59962022000400002&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN  Introducción: La esclerosis sistémica es una enfermedad rara de la cual existe información limitada en el Centro de Referencia de Enfermedades Reumáticas de La Habana.  Objetivo: Describir las características clínico-epidemiológicas, las comorbilidades asociadas y el tratamiento más utilizado de los pacientes atendidos en la institución.  Métodos: Se realizó un estudio observacional descriptivo, transversal de 73 pacientes con esclerosis sistémica en el periodo comprendido entre noviembre del año 2017 a marzo de 2019. Se evaluaron variables sociodemográficas como edad, sexo, color de la piel, nivel educacional y ocupación, y variables clínicas como forma de presentación y tiempo de diagnóstico de la enfermedad, manifestaciones clínicas, comorbilidades asociadas y tratamiento.  Resultados: El 57,5 % presentó la forma difusa de la enfermedad y el 48,8 % tenía más de 10 años de diagnóstico. La afectación digestiva apareció en el 94,5 %, la osteomioarticular en el 89,0 % y la cardiovascular en el 87,7 %. Estas afectaciones fueron las más representadas por órganos y sistemas. La hipertensión arterial seguida de la fibromialgia fueron las principales comorbilidades. Los anticálcicos, IECA, esteroides y el metotrexate fueron los fármacos más usados en el tratamiento.  Conclusiones: Predominó la forma difusa de la enfermedad, los enfermos con más de 10 años de diagnóstico y la afectación cutánea, digestiva y osteomioarticular. La hipertensión arterial seguida de la fibromialgia fueron las comorbilidades más identificadas.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT  Introduction:  Systemic sclerosis is a rare disease for which there is limited information in the Reference Center for Rheumatic Diseases of Havana.  Objective:  To describe the clinical-epidemiological characteristics of the patients treated with this diagnosis in the period from November 2017 to March 2019.  Methods:  A descriptive, cross-sectional observational study was carried out in 73 patients. Sociodemographic variables such as age, sex, skin color, educational level and occupation, clinical variables such as form of presentation and time of diagnosis of the disease, clinical manifestations, associated comorbidities and treatment were evaluated.  Results:  57.5% presented the diffuse form of the disease and 48.8% had more than 10 years of diagnosis. Digestive involvement in 94.5%, osteomyoarticular disease in 89.0%, and cardiovascular disease in 87.7% were the most represented by organs and systems. HT followed by fibromyalgia were the most identified comorbidities. Anti-calcium, ACEI, steroids and Methotrexate were the drugs most used in treatment.  Conclusions:  The diffuse form of the disease predominated, patients with more than 10 years of diagnosis and skin, digestive and osteomyoarticular involvement.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[esclerosis sistémica]]></kwd>
<kwd lng="es"><![CDATA[epidemiología]]></kwd>
<kwd lng="es"><![CDATA[manifestaciones clínicas]]></kwd>
<kwd lng="es"><![CDATA[comorbilidades]]></kwd>
<kwd lng="es"><![CDATA[tratamiento]]></kwd>
<kwd lng="en"><![CDATA[systemic sclerosis]]></kwd>
<kwd lng="en"><![CDATA[epidemiology]]></kwd>
<kwd lng="en"><![CDATA[clinical manifestations]]></kwd>
<kwd lng="en"><![CDATA[comorbidities]]></kwd>
<kwd lng="en"><![CDATA[treatment]]></kwd>
</kwd-group>
</article-meta>
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