<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1817-5996</journal-id>
<journal-title><![CDATA[Revista Cubana de Reumatología]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Cuba Reumatol]]></abbrev-journal-title>
<issn>1817-5996</issn>
<publisher>
<publisher-name><![CDATA[Editorial CIMEQ]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1817-59962023000400011</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Periarteritis/periaortitis y fibrosis retroperitoneal en enfermedad relacionada por IgG4]]></article-title>
<article-title xml:lang="en"><![CDATA[Periarteritis/periaortitis and retroperitoneal fibrosis in IgG4-related disease]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Paira]]></surname>
<given-names><![CDATA[Sergio]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Zunino]]></surname>
<given-names><![CDATA[Luisina]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Provincial Dr. José María Cullen  ]]></institution>
<addr-line><![CDATA[Santa Fe ]]></addr-line>
<country>Argentina</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2023</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2023</year>
</pub-date>
<volume>25</volume>
<numero>4</numero>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_arttext&amp;pid=S1817-59962023000400011&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_abstract&amp;pid=S1817-59962023000400011&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.sld.cu/scielo.php?script=sci_pdf&amp;pid=S1817-59962023000400011&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen La enfermedad relacionada a IGg4 es una afección fibroinflamatoria sistémica que cobra cada vez más relevancia. Se caracteriza por una triada clásica en el análisis histopatológico: Infiltrado linfoplasmocitario, fibrosis estoriforme y flebitis obliterante. El compromiso cardiovascular no queda fuera de su espectro pudiendo afectar a las arterias coronarias, las válvulas cardíacas, el miocardio, el pericardio, la aorta y la vasculatura periférica, confundiéndose con otras entidades reumatológicas que cursan con este compromiso. Resulta entonces fundamental reconocer las características clínicas e imagenológicas que la diferencian de las demás etiologías inflamatorias para su sospecha clínica y un óptimo accionar evitando complicaciones potencialmente fatales. La existencia de nuevos criterios órgano específicos pueden facilitar el diagnóstico de dicho compromiso. La afección vascular asociado con IgG4 puede causar complicaciones potencialmente mortales, como ruptura de aneurismática y estenosis arterial; sin embargo, los detalles de las características clínicas, el pronóstico y el tratamiento óptimo siguen sin ser claros debido a la rareza de esta afección.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract IGg4-related disease is a systemic fibroinflammatory disease that is becoming more relevant. It is characterized by a classic triad on histopathological analysis. Cardiovascular involvement does not go beyond its potential aspect to affect the coronary arteries, heart valves, myocardium, pericardium, aorta and peripheral vasculature, being confused with other rheumatological entities that suffer from this involvement. It is therefore essential to recognize the clinical and imaging characteristics that differentiate it from other inflammatory etiologies for clinical suspicion and better action to avoid potentially fatal complications. The existence of new organ-specific criteria may facilitate the diagnosis of this compromise, especially in patients with a high degree of success in obtaining tissue patterns. IgG4-associated vascular compromise can cause life-threatening complications, such as aneurysmal rupture and arterial stenosis; however, details of the clinical features, prediction, and optimal treatment will remain unclear due to the rarity of this condition.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[ER-IgG4]]></kwd>
<kwd lng="es"><![CDATA[aortitis]]></kwd>
<kwd lng="es"><![CDATA[periaortitis]]></kwd>
<kwd lng="en"><![CDATA[IgG4-RD]]></kwd>
<kwd lng="en"><![CDATA[aortitis]]></kwd>
<kwd lng="en"><![CDATA[periaortitis]]></kwd>
</kwd-group>
</article-meta>
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