Abstract

GOMEZ VIERA, Nelson; OLIVERA LEAL, Irma Regla; PARDO NUNEZ, Armando  and  MARTINEZ VALDES, Alexis. Stiff-man syndrome. Rev cubana med [online]. 2018, vol.57, n.1, pp. 55-60. ISSN 1561-302X.

Stiff-Man Syndrome is an uncommon and disturbing neurological disorder characterized by progressive contracture, stiffness and painful spasms that affect the axial musculature, making it impossible for the patient to walk around. We present a 22-year-old male patient with clinical and electromyographic manifestations compatible with this nosological disease. The treatment described for the disease did not produce an improvement in symptoms. Regarding the cases described in the scientific literature, this is the first patient diagnosed with Stiff-Man Syndrome who has received a dose of diazepam of 500 mg daily orally without adverse effects and a bolus dose of 800 mg of propofol to achieve muscle relaxation.

Keywords : stiff-man; muscle spasms; stiffness; spasmodic storm; diazepam; immunosuppression.

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