Abstract

ANDRADE LOTUFO, Mônica et al. Family nevus spongiosus albus. Rev Cubana Estomatol [online]. 2010, vol.47, n.2, pp. 260-265. ISSN 1561-297X.

The aim of present paper is to introduce three clinical cases from a family affected from nevus spongiosus albus (NSA) and also to discuss the possible differential diagnoses as well as the therapeutical behaviors to be adopted. Clinical case: A man aged 52 seen in our clinic due to bilateral white lesions noted 30 years ago without achieve a final diagnosis of lesions. After anamnesis and physical examination an incision biopsy was taken. The clinical and histopathological data collection allows making the NSA diagnosis. Thus, it was necessary to inquire again into the patient's relatives regarding the existence of similar lesions proving the presence of white plaques in oral mucosa in a son aged 19 and a daughter aged 25. The nevus spongiosus albus is an uncommon genetic lesion that must to be differentiated from other significant localized and systemic pathologies with serious repercussions for the subjects. Since there is not a curative treatment for the NSA, the role of the surgeon-dentist is to diagnose that lesion, to explain clearly to patient on the benign and self-limiting origin of this entity and if it is necessary from the aesthetic point of view, to apply the different therapeutical modalities to control the plaques.

Keywords : Hereditary mucous leucokeratosis; Cannon's nevus spongiosus albus; oral pathology.

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