Abstract

NIEVAS SANCHEZ, Marianne  and  TREVINO GONZALEZ, Julián. Hepatic Failure Secondary to Polycystic Renal-Hepatic Disease. Rev. Cuban de Med [online]. 2023, vol.62, n.2  Epub June 01, 2023. ISSN 1561-302X.

Autosomal dominant polycystic kidney disease is considered the most common genetic kidney disease and the fourth leading cause of chronic kidney disease worldwide. It affects about 1 in 1,000 live births. Polycystic liver disease is the most common extrarenal manifestation of polycystic kidney disease. Liver cirrhosis is a late finding in this disease and its presentation is more common in the elderly. Decompensation of the disease, with liver failure as the cause of death, is rare in polycystic liver disease. We report the case of a 60-year-old male patient with a personal pathological history of polycystic kidney disease with tense ascites and edema in both lower limbs, with evidence of liver failure and unfavorable evolution until his death. Although the presence of liver failure is associated with poor prognosis, its early detection may mean the initiation of timely and appropriate treatment that may be beneficial.

Keywords : polycystic kidney disease; liver cysts; liver failure.

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