Abstract

MOSQUERA BETANCOURT, Gretel; CORIMAYTA GUTIERREZ, Jasmany  and  TAMAKLOE, Kaffui. Monostotic fibrous dysplasia: a case report. AMC [online]. 2012, vol.16, n.5, pp. 620-627. ISSN 1025-0255.

Introduction: fibrous dysplasia is a rare disease that affects bones; it is characterized by the replacement of normal bony tissue by immature fibrous tissue, with increased incidence during adolescence and in the female sex. It may be monostotic or polyostotic depending on the condition of one or more bones involved and it has generally a benign course. Imaging studies suggest diagnosis that must be confirmed by anatomopathologic study. There is no a specific drug treatment currently.      Clinical Case:  an 18-year-old patient admitted in the Neurosurgery Unit at the University Hospital Manuel Ascunce Domnech presented moderate headache, an increase in volume at the level of the left frontal region was found. With the presumptive diagnosis of monostotic fibrous dysplasia was performed simple X-ray and computerized axial tomography, where was evidenced the existence of single tumor lesion at the level of the right frontal and orbital region, extending to the anterior skull base that increased the diameter of these bones of fibrous dysplasia. The collective and multidisciplinary discussion of the case suggested a conservative treatment taking into account the extension of the lesion to the cranial base. Conclusions: monostotic fibrous dysplasia of the skull is a benign disease of unknown cause, whose clinical presentation depends on its location. Surgical treatment is recommended in cases where it is possible to perform complete exeresis of the lesion.

Keywords : FIBROUS DYSPLASIA, MONOSTOTIC; BONE AND BONES; DIAGNOSIS, DIFFERENTIAL; SURGICAL PROCEDURES, OPERATIVE; CASE STUDIES; ADOLESCENT.

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