Abstract

ROMERO GARCIA, Armando et al. Brugada Syndrome. Report of a Case. CCM [online]. 2014, vol.18, n.2, pp. 363-371. ISSN 1560-4381.

Brugada syndrome is a clinical-electrocardiographic manifestation characterized by a mutation of the cardiac sodium channel, more common in males, that is characterized by recurrent episodes of syncope and sudden death in patients without apparent structural heart disease. The typical pattern is characterized by an image of right bundle branch block with ST elevation in V1 to V3 and T negative. It is vital to the diagnosis of this syndrome because without treatment the incidence of sudden death is very high, the implantation of an automatic defibrillator is the only useful treatment. A young woman aged 32 attended by recurrent presyncopal episodes was reported in this article. The patient presented normal baseline electrocardiograms, with hidden or intermittent pattern of Brugada type I. The procainamide test was positive and electrophysiological study was negative, a cardioverter defibrillator was implanted.

Keywords : Brugada syndrome; polymorphic ventricular tachycardia; ventricular fibrillation; sudden death; defibrillator.

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