Abstract

AGUADO BARRENA, Obdulia María; BERMUDEZ BERMUDEZ, Stella Milena  and  RODRIGUEZ RAMIREZ, Carlos. Anaesthesia in a spinal column arthodesis secondary to Marfan Syndrome. Rev cuba anestesiol reanim [online]. 2013, vol.12, n.1, pp. 46-51. ISSN 1726-6718.

Background: Marfan Syndrome is a hereditary disorder of the conjunctive tissue that presents with valve diseases, aneurism of the thoracic aeorta and articular lax of the skeleton. Patients can present important respiratory problems such as the restraint of the pulmonary function due to both alterations in the thoracic wall and Kyphoscoliosis that require surgical correction. Objectives: To show an anaesthetic behaviour in a patient that presented to hospital for a surgical correction of scoliosis secondary to Marfan Syndrome. Methods: General anaesthesia with the total intravenous technique with Propofol, Fentanyl and Vecuronio was given after an adequate preoperative assessment. Controlled hypotension and antifibrinolitics were used as blood-saving techniques and intrathecal Morphine was administered which, apart from providing an adequate postoperative analgesia, contributed to the controlled hypotension technique. Results: The patient presented neither surgical complications nor anaesthetic ones. Bleeding was of 1 000 mL. Good analgesic conditions were obtained during the postoperative phase. Conclusions: In a patient suffering from Marfan Syndrome, the preoperative evaluation should be focused to both respiratory and cardiovascular alterations. Adequeate analgesic conditions were obtained with the administration of intrathecal Morphine.

Keywords : Marfan Syndrome; scoliosis; controlled hypotension; intrathecal Morphine.

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