Abstract

AMORES AGULLA, Tania; CANTERO DOMINGUEZ, Yania  and  MARRERO QUESADA, José. Anaesthesia in Steinert Disease. Rev cuba anestesiol reanim [online]. 2013, vol.12, n.1, pp. 52-56. ISSN 1726-6718.

Background: Steinert´s myotonic dystrophy is a hereditary chronic multisystemic process that principally affects skeletal muscles and presents with slowly progressive myotony and muscular atrophies. Patients suffering from this disease are very susceptible to anaesthetic agents and can present serious perioperative complications. Objectives: To describe the surgical evolution of a patient suffering from Steinert´s disease. Clinical case report: A 42-year-old female patient that has been presenting metrorrhagias and dysmenorrheas of more than two years of evolution was operated on uterine fibroma. She had personal pathological antecedents of Steinert´s disease of fifteen years evolution and symptoms that worsened after delivery. Conclusions: The patients who suffer from Steinert´s disease represent a challenge for the anaesthesiologist; nevertheless, an individualized and detailed preoperative assessment in each case so as the benefits offered by the monitoring, anaesthetic and surgical techniques allow a satisfactory evolution.

Keywords : Steinert´s disease; myotonic dystrophy; myotony.

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