Abstract

SORIA LOPEZ, Juan Antonio et al. Report and discussion of a case with Cantrell's Pentalogy. Rev Cubana Obstet Ginecol [online]. 2004, vol.30, n.2, pp. 0-0. ISSN 1561-3062.

It is a rare syndrome characterized by a disruption in the low sternum, ectopia cordis, anterior defects of the diaphragm, defects in the supraumbilical anterior abdominal wall, defects in the diaphragmatic pericardium and heart anomalies. It was reported the case of a 28-year-old primigravida with echosonography that shows a defect in the abdominal thoracic wall with protrusion of the intestinal loops (omphalocele) and ectopia cardis, that is diagnosed Cantrell's pentalogy. It was obtained a male product of 32 weeks of gestation and 1700 g, with omphalocele, ectopia cordis and defect of the lower segment of the sternum, that died a few hours later.

Keywords : Cantrell's pentalogy; ectopia cordis; ultrasonographic diagnosis; treatment.