Abstract

VEGA BETANCOURT, Nuria; JIMENEZ PUNALES, Sandi  and  RODRIGUEZ SANTOS, Irene C. Botryoid Rhabdomyosarcoma of the Female Genital Tract in a Virgin Adolescent. Rev Cubana Obstet Ginecol [online]. 2018, vol.44, n.4, pp. 1-8. ISSN 1561-3062.

Rhabdomyosarcoma is a complex and highly malignant tumor that originates in the cells of the embryonic mesenchyme with the ability to differentiate into skeletal muscle cells. This is the most common malignant soft tissue tumor. It represents approximately 3.5% of cancer cases in children from zero to 14 years of age. A case of a virgin adolescent patient is presented. A botryoid rhabdomyosarcoma of the vagina was diagnosed histologically. The clinical presentation of embryonic botryoid rhabdomyosarcoma variety is, in general, a mass that protrudes through the urethra or vaginal introitus, or the presence of fetid flow or vaginal bleeding in girls under 2 years. In these lesions, diagnostic support with immunohistochemistry is of vital importance. The prognosis of this disease is determined by variables such as tumor size, compromised organ, age of the patient, surgical result (R0 / R1) and presence of metastasis. Early and timely multidisciplinary medical evaluation will always allow an adequate diagnosis and treatment to be established.

Keywords : rhabdomyosarcoma; botryoid tumor; vagina.

        · abstract in Spanish     · text in Spanish     · Spanish ( pdf )