Resumo

RUIZ-BOTERO, Felipe; QUINTANA PENA, Valentina  e  PACHAJOA, Harry. Poland sequence, going from the embryological bases to the clinical practice. Rev Cubana Pediatr [online]. 2015, vol.87, n.2, pp. 241-246. ISSN 1561-3119.

Poland sequence is a birth defect typically described as unilateral congenital absence of the pectoralis muscle, which may be associated with the occurrence of other ipsilateral thoracic and/or upper extremities anomalies that cover different degrees of functional severity and esthetic alterations. The literature describes various types of association with different syndromes; however, its etiology remains unknown and several hypotheses about the possible cause of this disease exist, being the most accepted the one that deals with vascular disruption processes. In the clinical practice, mild forms of expression can be ignored, but in the most severe cases, the attention of a multidisciplinary group of specialists is required for disease management. A systematic literature review on Poland sequence was made.

Palavras-chave : Poland sequence; birth defect; thoracic wall; subclavian artery; sternum; pectoralis muscles.

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